Defective organellar acidification as a cause of cystic fibrosis lung disease: Reexamination of a recurring hypothesis

American Journal of Physiology - Lung Cellular and Molecular Physiology

Volumn 296, Issue 6, 2009, Pages

  Haggie, Peter M ^a   Verkman, A S ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

Chloride channel; Cystic fibrosis transmembrane conductance regulator; Endosome; Golgi; Lysosome

Indexed keywords

CERAMIDE; CHLORIDE CHANNEL; TRANSMEMBRANE CONDUCTANCE REGULATOR;

ACIDIFICATION; ANTIMICROBIAL ACTIVITY; CLINICAL EXAMINATION; ENDOSOME; GOLGI COMPLEX; HUMAN; HYPOTHESIS; LUNG ALVEOLUS MACROPHAGE; LUNG FIBROSIS; LYSOSOME; NEUTROPHIL; NONHUMAN; PATHOGENESIS; PHAGOLYSOSOME; PRIORITY JOURNAL; PROTEIN PROCESSING; REVIEW; SODIUM TRANSPORT;

ACID-BASE EQUILIBRIUM; ACIDS; ANIMALS; CYSTIC FIBROSIS; HUMANS; LUNG; ORGANELLES;

EID: 67049172475     PISSN: 10400605     EISSN: 15221504     Source Type: Journal    
DOI: 10.1152/ajplung.00018.2009     Document Type: Review

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