Physiological functions of CLC Cl- channels gleaned from human genetic disease and mouse models

Annual Review of Physiology

Volumn 67, Issue , 2005, Pages 779-807

  Jentsch, Thomas J ^a   Poët, Mallorie ^a   Fuhrmann, Jens C ^a   Zdebik, Anselm A ^a  

^a UNIVERSITY OF HAMBURG   (Germany)

Author keywords

Anion channels; Cystic fibrosis; Endocytosis; Transepithelial transport; Volume regulation

Indexed keywords

CHLORIDE CHANNEL;

ACIDIFICATION; ALBERS SCHOENBERG DISEASE; ANIMAL MODEL; BARTTER SYNDROME; BARTTIN GENE; BLINDNESS; CELL MEMBRANE; CELL ORGANELLE; CIC 1 GENE; CLC 2 GENE; CLC 3 GENE; CLC 5 GENE; CLC 7 GENE; CLC GENE; CLC K GENE; DEGENERATIVE DISEASE; DENT DISEASE; ELECTRIC POTENTIAL; ENDOSOME; EPILEPSY; EPITHELIUM; FLUID TRANSPORT; GENE; GENE DISRUPTION; GENE MUTATION; GENETIC DISORDER; HEARING IMPAIRMENT; INFERTILITY; LYSOSOME; MAMMAL; MYOTONIA; NEPHROLITHIASIS; NERVE CELL; OSTEOCLAST; PHENOTYPE; PRIORITY JOURNAL; PROTEINURIA; REVIEW; SYNAPSE VESICLE;

ANIMALS; CHLORIDE CHANNELS; DISEASE MODELS, ANIMAL; GENETIC DISEASES, INBORN; HUMANS; MICE; MULTIGENE FAMILY;

EID: 15544362767     PISSN: 00664278     EISSN: None     Source Type: Book Series    
DOI: 10.1146/annurev.physiol.67.032003.153245     Document Type: Review

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