N-Glycosylation Is Crucial for Folding, Trafficking, and Stability of Human Tripeptidyl-peptidase I

Journal of Biological Chemistry

Volumn 279, Issue 13, 2004, Pages 12827-12839

  Wujek, Peter ^a   Kida, Elizabeth ^a   Walus, Marius ^a   Wisniewski, Krystyna E ^a   Golabek, Adam A ^a  

^a NEW YORK STATE INSTITUTE FOR BASIC RESEARCH IN DEVELOPMENTAL DISABILITIES   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

BIOLOGICAL ORGANS; CELLS; DNA; NEUROLOGY; PH EFFECTS; POLYPEPTIDES; THERMODYNAMIC STABILITY;

N-GLYCOSYLATION; TRAFFICKING;

ENZYMES;

COMPLEMENTARY DNA; PEPTIDASE; POLYPEPTIDE; PROTON TRANSPORTING ADENOSINE TRIPHOSPHATE SYNTHASE; TRIPEPTIDYL PEPTIDASE I; UNCLASSIFIED DRUG;

ACIDIFICATION; ARTICLE; CELL FATE; CHO CELL; DISULFIDE BOND; ENDOPLASMIC RETICULUM; ENZYME ACTIVITY; ENZYME INACTIVATION; ENZYME RELEASE; ENZYME STABILITY; GLYCOSYLATION; HUMAN; HUMAN CELL; LIPOFUSCINOSIS; LYSOSOME MEMBRANE; MISSENSE MUTATION; PRIORITY JOURNAL; PROTEIN FOLDING; THERMOSTABILITY;

ANIMALS; ASPARAGINE; BINDING SITES; BLOTTING, WESTERN; CELL LINE; CHO CELLS; CRICETINAE; DISULFIDES; DNA, COMPLEMENTARY; ELECTROPHORESIS, POLYACRYLAMIDE GEL; ENDOPEPTIDASES; ENDOPLASMIC RETICULUM; GLYCOSYLATION; HUMANS; HYDROGEN-ION CONCENTRATION; MANNOSE; MICROSCOPY, FLUORESCENCE; MUTAGENESIS, SITE-DIRECTED; MUTATION; MUTATION, MISSENSE; POLYSACCHARIDES; PRECIPITIN TESTS; PROTEIN BINDING; PROTEIN CONFORMATION; PROTEIN FOLDING; PROTEIN TRANSPORT; TEMPERATURE; TIME FACTORS; TRANSFECTION;

CRICETINAE; CRICETULUS GRISEUS;

EID: 1842581899     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.M313173200     Document Type: Article

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