Different patterns of hydrophobic protein storage in different forms of neuronal ceroid lipofuscinosis (NCL, Batten disease)

Neuropediatrics

Volumn 28, Issue 1, 1997, Pages 45-48

  Palmer, D N ^a   Jolly, R D ^b   Van Mil, H C ^a   Tyynela J ^c   Westlake, V J ^b  

^a LINCOLN UNIVERSITY   (New Zealand)

^b MASSEY UNIVERSITY   (New Zealand)

^c UNIVERSITY OF HELSINKI   (Finland)

Author keywords

Activator proteins; ATP synthase; SAPs; Subunit C sphingolipid; Vacuolar ATPase

Indexed keywords

ANTIBODY; PROTEIN; PROTON TRANSPORTING ADENOSINE TRIPHOSPHATE SYNTHASE; SPHINGOLIPID ACTIVATOR PROTEIN;

ANIMAL TISSUE; ARTICLE; BIOACCUMULATION; DOG; ENZYME SUBUNIT; HUMAN; MITOCHONDRION; MOUSE; NEURONAL CEROID LIPOFUSCINOSIS; NONHUMAN; PRIORITY JOURNAL; SHEEP; STORAGE;

EID: 0030845481     PISSN: 0174304X     EISSN: None     Source Type: Journal    
DOI: 10.1055/s-2007-973666     Document Type: Article

References (23)

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