Human acid ceramidase: Processing, glycosylation, and lysosomal targeting

Journal of Biological Chemistry

Volumn 276, Issue 38, 2001, Pages 35352-35360

  Ferlinz, Klaus ^a   Kopal, Guido ^b   Bernardo, Katussevani ^b,e   Linke, Thomas ^b   Bär, Julia ^b   Breiden, Bernadette ^b   Neumann, Ulrich ^c   Lang, Florian ^a   Schuchman, Edward H ^d   Sandhoff, Konrad ^a,b  

^a UNIVERSITY OF TÜBINGEN   (Germany)

^b UNIVERSITY OF BONN   (Germany)

^c UNIVERSITY OF VETERINARY MEDICINE HANNOVER   (Germany)

^d MOUNT SINAI SCHOOL OF MEDICINE   (United States)

^e Institute of Medical Microbiology Immunology and Hygiene   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

BIOSYNTHESIS; CARBOHYDRATES; CATALYST ACTIVITY; CELLS; DNA; ORGANIC ACIDS; POLYPEPTIDES;

ENDOCYTOSIS; FIBROBLASTS;

ENZYMES;

ACYLSPHINGOSINE DEACYLASE; AMMONIUM CHLORIDE; CARBOHYDRATE; COMPLEMENTARY DNA; SOMATOMEDIN B RECEPTOR; GALACTOSYLGALACTOSYLGLUCOSYLCERAMIDASE; PRIMER DNA;

ANIMAL CELL; ARTICLE; BIOSYNTHESIS; ENDOCYTOSIS; ENDOSOME; ENZYME ACTIVITY; ENZYME RELEASE; ENZYME SYNTHESIS; FIBROBLAST; HUMAN; HUMAN CELL; LYSOSOME; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN GLYCOSYLATION; PROTEIN PROCESSING; PROTEIN TARGETING; SITE DIRECTED MUTAGENESIS; ANIMAL; CELL CULTURE; CELL STRAIN COS1; DRUG EFFECT; ENZYMOLOGY; GENETICS; GLYCOSYLATION; METABOLISM; NUCLEOTIDE SEQUENCE; PROTEIN TRANSPORT;

ANIMALIA;

AMMONIUM CHLORIDE; ANIMALS; BASE SEQUENCE; CELLS, CULTURED; CERAMIDE TRIHEXOSIDASE; COS CELLS; DNA PRIMERS; DNA, COMPLEMENTARY; ENDOCYTOSIS; FIBROBLASTS; GLYCOSYLATION; HUMANS; LYSOSOMES; PROTEIN PROCESSING, POST-TRANSLATIONAL; PROTEIN TRANSPORT; RECEPTOR, IGF TYPE 2;

EID: 0035929560     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.M103066200     Document Type: Article

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