Proteasome inhibition enhances the stability of mouse Cu/Zn superoxide dismutase with mutations linked to familial amyotrophic lateral sclerosis

Journal of the Neurological Sciences

Volumn 139, Issue 1, 1996, Pages 15-20

  Hoffman, Eric K ^a   Wilcox, Heide M ^a   Scott, Richard W ^a   Siman, Robert ^a  

^a CEPHALON INC   (United States)

Author keywords

Amyotrophic lateral sclerosis; Cu Zn superoxide dismutase; Proteasome; Proteasome inhibitor; Proteolytic degradation; SOD1 mutations

Indexed keywords

COPPER ZINC SUPEROXIDE DISMUTASE; PROTEASOME;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL TISSUE; ARTICLE; CELL CULTURE; CONTROLLED STUDY; GENETIC TRANSFECTION; HUMAN; HUMAN CELL; KIDNEY CELL; MOUSE; NONHUMAN; POINT MUTATION; PRIORITY JOURNAL;

EID: 0030200643     PISSN: 0022510X     EISSN: None     Source Type: Journal    
DOI: 10.1016/0022-510X(96)00031-7     Document Type: Article

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