Mammalian osmolytes and S-nitrosoglutathione promote ΔF508 cystic fibrosis transmembrane conductance regulator (CFTR) protein maturation and function

Journal of Biological Chemistry

Volumn 278, Issue 37, 2003, Pages 35159-35167

  Howard, Marybeth ^a   Fischer, Horst ^c   Roux, Jeremie ^b   Santos, Bento C ^d   Gullans, Steven R ^e   Yancey, Paul H ^f   Welch, William J ^a,b  

^a UNIVERSITY OF CALIFORNIA   (United States)

^b UNIVERSITY OF CALIFORNIA   (United States)

^c CHILDREN S HOSPITAL OAKLAND RESEARCH INSTITUTE   (United States)

^d FEDERAL UNIVERSITY OF SÃO PAULO   (Brazil)

^e BRIGHAM AND WOMEN S HOSPITAL   (United States)

^f WHITMAN COLLEGE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CELL MEMBRANES; CELLS; HIGH PERFORMANCE LIQUID CHROMATOGRAPHY; PATIENT TREATMENT;

HYPEROSMOTIC STRESS;

PROTEINS;

GAMMA GLUTAMYLTRANSFERASE; GLYCEROPHOSPHORYLCHOLINE; INOSITOL; S NITROSOGLUTATHIONE; SORBITOL; TAURINE; TRANSMEMBRANE CONDUCTANCE REGULATOR; UREA;

ANIMAL CELL; ARTICLE; CELL CULTURE; CELL GROWTH; CELL LYSATE; CELL MEMBRANE; CONTROLLED STUDY; ENZYME SUBSTRATE; GENE CONTROL; GENE MUTATION; HIGH PERFORMANCE LIQUID CHROMATOGRAPHY; HOMOZYGOSITY; HYPEROSMOLALITY; INTESTINE MUCOSA; KIDNEY CELL; KIDNEY DYSFUNCTION; MOUSE; MUCUS SECRETION; NONHUMAN; OSMOTIC STRESS; PATCH CLAMP; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN FOLDING; PROTEIN FUNCTION; PROTEIN PROCESSING; PROTEIN STABILITY; RESPIRATORY TRACT MUCOSA;

3T3 CELLS; ANIMALS; BETAINE; CELLS, CULTURED; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; INOSITOL; KIDNEY TUBULES, COLLECTING; MAMMALS; MICE; NITRIC OXIDE DONORS; OSMOLAR CONCENTRATION; PATCH-CLAMP TECHNIQUES; S-NITROSOGLUTATHIONE; SEQUENCE DELETION; SORBITOL; STRESS, MECHANICAL; TAURINE; TRANSFECTION;

ANIMALIA; MAMMALIA;

EID: 0042317083     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.M301924200     Document Type: Article

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