-
2
-
-
0032472239
-
BSE and prions: Uncertainties about the agent
-
(1998)
Science
, vol.279
, pp. 42-43
-
-
Chesebro, B.1
-
3
-
-
0020321767
-
Novel proteinaceous infectious particles cause scrapie
-
(1982)
Science
, vol.216
, pp. 136-144
-
-
Prusiner, S.B.1
-
4
-
-
0022476747
-
Scrapie and cellular PrP isoforms are encoded by the same chromosomal gene
-
(1986)
Cell
, vol.46
, pp. 417-428
-
-
Basler, K.1
Oesch, B.2
Scott, M.3
Westaway, D.4
Walchli, M.5
Groth, D.F.6
McKinley, M.P.7
Prusiner, S.B.8
Weissmann, C.9
-
5
-
-
0021884354
-
Identification of scrapie prion protein-specific mRNA in scrapie-infected and uninfected brain
-
(1985)
Nature
, vol.315
, pp. 331-333
-
-
Chesebro, B.1
Race, R.2
Wehrly, K.3
Nishio, J.4
Bloom, M.5
Lechner, D.6
Bergstrom, S.7
Robbins, K.8
Mayer, L.9
Keith, J.M.10
-
6
-
-
0026600865
-
Normal development and behaviour of mice lacking the neuronal cell-surface PrP protein
-
(1992)
Nature
, vol.356
, pp. 577-582
-
-
Bueler, H.R.1
Fischer, M.2
Lang, Y.3
Bluethmann, H.4
Lipp, H.P.5
DeArmond, S.J.6
Prusiner, S.B.7
Aguet, M.8
Weissmann, C.9
-
9
-
-
0030775632
-
Transmissions to mice indicate that 'new variant' CJD is caused by the BSE agent
-
[see comments].
-
(1997)
Nature
, vol.389
, pp. 498-501
-
-
Bruce, M.E.1
Will, R.G.2
Ironside, J.W.3
McConnell, I.4
Drummond, D.5
Suttie, A.6
McCardle, L.7
Chree, A.8
Hope, J.9
Birkett, C.10
Cousens, S.11
Fraser, H.12
Bostock, C.J.13
-
10
-
-
0030820354
-
The same prion strain causes vCJD and BSE
-
[letter] [see comments].
-
(1997)
Nature
, vol.389
, pp. 448-450
-
-
Hill, A.F.1
Desbruslais, M.2
Joiner, S.3
Sidle, K.C.4
Gowland, I.5
Collinge, J.6
Doey, L.J.7
Lantos, P.8
-
20
-
-
0025869213
-
Mutation of the prion protein in Libyan Jews with Creutzfeldt-Jakob disease
-
(1991)
N. Engl. J. Med.
, vol.324
, pp. 1091-1097
-
-
Hsiao, K.1
Meiner, Z.2
Kahana, E.3
Cass, C.4
Kahana, I.5
Avrahami, D.6
Scarlato, G.7
Abramsky, O.8
Prusiner, S.B.9
Gabizon, R.10
-
23
-
-
0033485260
-
A single amino acid alteration (101L) introduced into murine PrP dramatically alters incubation time of transmissible spongiform encephalopathy
-
(1999)
EMBO J.
, vol.18
, pp. 6855-6864
-
-
Manson, J.C.1
Jamieson, E.2
Baybutt, H.3
Tuzi, N.L.4
Barron, R.5
McConnell, I.6
Somerville, R.7
Ironside, J.8
Will, R.9
Sy, M.S.10
Melton, D.W.11
Hope, J.12
Bostock, C.13
-
26
-
-
0030878056
-
Recombinant full-length murine prion protein, mPrP(23-231): Purification and spectroscopic characterization
-
(1997)
FEBS Lett.
, vol.413
, pp. 277-281
-
-
Hornemann, S.1
Korth, C.2
Oesch, B.3
Riek, R.4
Wider, G.5
Wuthrich, K.6
Glockshuber, R.7
-
28
-
-
0027332116
-
Conversion of alpha-helices into beta-sheets features in the formation of the scrapie prion proteins
-
(1993)
Proc. Natl. Acad. Sci. U.S.A.
, vol.90
, pp. 10962-10966
-
-
Pan, K.M.1
Baldwin, M.2
Nguyen, J.3
Gasset, M.4
Serban, A.5
Groth, D.6
Mehlhorn, I.7
Huang, Z.8
Fletterick, R.J.9
Cohen, F.E.10
-
29
-
-
0028882424
-
Prion propagation in mice expressing human and chimeric PrP transgenes implicates the interaction of cellular PrP with another protein
-
(1995)
Cell
, vol.83
, pp. 79-90
-
-
Telling, G.C.1
Scott, M.2
Mastrianni, J.3
Gabizon, R.4
Torchia, M.5
Cohen, F.E.6
DeArmonds, S.J.7
Prusiner, S.B.8
-
30
-
-
0027195933
-
Seeding 'one-dimensional crystallization' of amyloid: A pathogenic mechanism in Alzheimer's disease and scrapie?
-
(1993)
Cell
, vol.73
, pp. 1055-1058
-
-
Jarrett, J.T.1
Lansbury P.T., Jr.2
-
35
-
-
0344222186
-
Selective neuronal targeting in prion disease
-
(1997)
Neuron
, vol.19
, pp. 1337-1348
-
-
DeArmond, S.J.1
Sanchez, H.2
Yehiely, F.3
Qiu, Y.4
Ninchak-Casey, A.5
Daggett, V.6
Camerino, A.P.7
Cayetano, J.8
Rogers, M.9
Groth, D.10
Torchia, M.11
Tremblay, P.12
Scott, M.R.13
Cohen, F.E.14
Prusiner, S.B.15
-
41
-
-
0027466091
-
Immunologic and molecular biologic studies of prion proteins in bovine spongiform encephalopathy
-
(1993)
J. Infect. Dis.
, vol.167
, pp. 602-613
-
-
Prusiner, S.B.1
Fuzi, M.2
Scott, M.3
Serban, D.4
Serban, H.5
Taraboulos, A.6
Gabriel, J.M.7
Wells, G.A.8
Wilesmith, J.W.9
Bradley, R.10
-
42
-
-
0024530897
-
Insertion in prion protein gene in familial Creutzfeldt-Jakob disease
-
[letter].
-
(1989)
Lancet
, vol.1
, pp. 51-52
-
-
Owen, F.1
Poulter, M.2
Lofthouse, R.3
Collinge, J.4
Crow, T.J.5
Risby, D.6
Baker, H.F.7
Ridley, R.M.8
Hsiao, K.9
Prusiner, S.B.10
-
43
-
-
0024474822
-
Diagnosis of Gerstmann-Straussler syndrome in familial dementia with prion protein gene analysis
-
(1989)
Lancet
, vol.2
, pp. 15-17
-
-
Collinge, J.1
Harding, A.E.2
Owen, F.3
Poulter, M.4
Lofthouse, R.5
Boughey, A.M.6
Shah, T.7
Crow, T.J.8
-
45
-
-
0026567814
-
Nearly ubiquitous tissue distribution of the scrapie agent precursor protein
-
(1992)
Neurology
, vol.42
, pp. 149-156
-
-
Bendheim, P.E.1
Brown, H.R.2
Rudelli, R.D.3
Scala, L.J.4
Goller, N.L.5
Wen, G.Y.6
Kascsak, R.J.7
Cashman, N.R.8
Bolton, D.C.9
-
46
-
-
0030940607
-
Identification of candidate proteins binding to prion protein
-
(1997)
Neurobiol. Dis.
, vol.3
, pp. 339-355
-
-
Yehiely, F.1
Bamborough, P.2
Da Costa, M.3
Perry, B.J.4
Thinakaran, G.5
Cohen, F.E.6
Carlson, G.A.7
Prusiner, S.B.8
-
48
-
-
0031466157
-
Complementary hydropathy identifies a cellular prion protein receptor
-
[see comments].
-
(1997)
Nat. Med.
, vol.3
, pp. 1376-1382
-
-
Martins, V.R.1
Graner, E.2
Gacia-Abreu, J.3
de Souza, S.J.4
Mercadante, A.F.5
Veiga, S.S.6
Zanata, S.M.7
Neto, V.M.8
Brentani, R.R.9
-
49
-
-
0031753397
-
Complete genomic sequence and analysis of the prion protein gene region from three mammalian species
-
(1998)
Genome Res.
, vol.8
, pp. 1022-1037
-
-
Lee, I.Y.1
Westaway, D.2
Smit, A.F.3
Wang, K.4
Seto, J.5
Chen, L.6
Acharya, C.7
Ankener, M.8
Baskin, D.9
Cooper, C.10
Yao, H.11
Prusiner, S.B.12
Hood, L.E.13
-
51
-
-
0028820122
-
Accumulation of proteinase K-resistant prion protein (PrP) is restricted by the expression level of normal PrP in mice inoculated with a mouse-adapted strain of the Creutzfeldt-Jakob disease agent
-
(1995)
J. Virol.
, vol.69
, pp. 7586-7592
-
-
Sakaguchi, S.1
Katamine, S.2
Shigematsu, K.3
Nakatani, A.4
Moriuchi, R.5
Nishida, N.6
Kurokawa, K.7
Nakaoke, R.8
Sato, H.9
Jishage, K.10
-
52
-
-
13344282734
-
Loss of cerebellar purkinje cells in aged mice homozygous for a disrupted PrP gene
-
(1996)
Nature
, vol.380
, pp. 528-531
-
-
Sakaguchi, S.1
Katamine, S.2
Nishida, N.3
Moriuchi, R.4
Shigematzu, K.5
Sugimoto, T.6
Nakatni, A.7
Kataoka, Y.8
Houtani, H.9
Shirabe, S.10
Okada, H.11
Hasegawa, S.12
Myamoto, T.13
Noda, T.14
-
53
-
-
0033049539
-
A mouse prion protein transgene rescues mice deficient for the prion protein gene from purkinje cell degeneration and demyelination
-
(1999)
Lab. Invest.
, vol.79
, pp. 689-697
-
-
Nishida, N.1
Tremblay, P.2
Sugimoto, T.3
Shigematsu, K.4
Shirabe, S.5
Petromilli, C.6
Erpel, S.P.7
Nakaoke, R.8
Atarashi, R.9
Houtani, T.10
Torchia, M.11
Sakaguchi, S.12
DeArmond, S.J.13
Prusiner, S.B.14
Katamine, S.15
-
54
-
-
0033215478
-
Ataxia in prion protein (PrP)-deficient mice is associated with upregulation of the novel PrP-like protein doppel
-
[In Process Citation]
-
(1999)
J. Mol. Biol.
, vol.292
, pp. 797-817
-
-
Moore, R.C.1
Lee, I.Y.2
Silverman, G.L.3
Harrison, P.M.4
Strome, R.5
Heinrich, C.6
Karunaratne, A.7
Pasternak, S.H.8
Chishti, M.A.9
Liang, Y.10
Mastrangelo, P.11
Wang, K.12
Smit, A.F.13
Katamine, S.14
Carlson, G.A.15
Cohen, F.E.16
Prusiner17
Hood, L.E.18
Westaway, D.19
-
55
-
-
0001552281
-
Expression of amino-terminally truncated PrP in the mouse leading to ataxia and specific cerebellar lesions
-
(1998)
Cell
, vol.93
, pp. 203-214
-
-
Shmerling, D.1
Hegyi, I.2
Fischer, M.3
Blattler, T.4
Brandner, S.5
Gotz, J.6
Rulicke, T.7
Flechsig, E.8
Cozzio, A.9
von Mering, C.10
Hangartner, C.11
Aguzzi, A.12
Weissmann, C.13
-
57
-
-
0033576378
-
Spongiform encephalopathies. Breech-birth prions
-
[news; comment]
-
(1999)
Nature
, vol.402
, pp. 737-739
-
-
Hope, J.1
-
58
-
-
0028911161
-
The cellular prion protein (PrP) selectively binds to Bcl-2 in the yeast two-hybrid system. Identification of candidate proteins binding to prion protein
-
(1995)
Brain. Res. Mol. Brain. Res.
, vol.30
, pp. 165-168
-
-
Kurschner, C.1
Morgan, J.I.2
Yehiely, F.3
Bamborough, P.4
Da Costa, M.5
Perry, B.J.6
Thinakarin, G.7
Cohen, F.E.8
Carlson, G.A.9
Prusiner, S.B.10
-
61
-
-
0033566067
-
Prions prevent neuronal cell-line death
-
[letter]
-
(1999)
Nature
, vol.400
, pp. 225-226
-
-
Kuwahara, C.1
Takeuchi, A.M.2
Nishimura, T.3
Haraguchi, K.4
Kubosaki, A.5
Matsumoto, Y.6
Saeki, K.7
Yokoyama, T.8
Itohara, S.9
Onodera, T.10
-
62
-
-
0013894656
-
The relative suceptibility of sheep, goats and mice to two types of the goat scrapie agent
-
(1966)
Res. Vet. Sci.
, vol.7
, pp. 207-212
-
-
Pattison, I.H.1
-
63
-
-
0024820814
-
Transgenic mice expressing hamster prion protein produce species-specific scrapie infectivity and amyloid plaques
-
(1989)
Cell
, vol.59
, pp. 847-857
-
-
Scott, M.1
Foster, D.2
Mirenda, C.3
Serban, D.4
Coufal, F.5
Walchli, M.6
Torchia, M.7
Groth, D.8
Carlson, G.9
DeArmond, S.J.10
-
64
-
-
0025244011
-
Transgenic studies implicate interactions between homologous PrP isoforms in scrapie prion replication
-
(1990)
Cell
, vol.63
, pp. 673-686
-
-
Prusiner, S.B.1
Scott, M.2
Foster, D.3
Pan, K.M.4
Groth, D.5
Mirenda, C.6
Torchia, M.7
Yang, S.L.8
Serban, D.9
Carlson, G.A.10
-
66
-
-
0001031163
-
The basis of strain variation in scrapie
-
Prusiner SB, Collinge J, Powell J anderton B, eds. Prion Diseases of Humans and Animals. New York, London: Ellis Horwood
-
(1992)
, pp. 497-508
-
-
Bruce, M.E.1
Fraser, H.2
McBride, P.A.3
Scott, J.R.4
Dickinson, A.G.5
-
67
-
-
0028043661
-
Distinct PrP properties suggest the molecular basis of strain variation in transmissible mink encephalopathy
-
(1994)
J. Virol.
, vol.68
, pp. 7859-7868
-
-
Bessen, R.A.1
Marsh, R.F.2
-
68
-
-
12644272790
-
Evidence for the conformation of the pathologic isoform of the prion protein enciphering and propagating prion diversity
-
[see comments]
-
(1996)
Science
, vol.274
, pp. 2079-2082
-
-
Telling, G.C.1
Parchi, P.2
DeArmond, S.J.3
Cortelli, P.4
Montagna, P.5
Gabizon, R.6
Mastrianni, J.7
Lugaresi, E.8
Gambetti, P.9
Prusiner, S.B.10
-
69
-
-
0031720905
-
Eight prion strains have PrP(Sc) molecules with different conformations
-
[see comments]
-
(1998)
Nat. Med.
, vol.4
, pp. 1157-1165
-
-
Safar, J.1
Wille, H.2
Itri, V.3
Groth, D.4
Serban, H.5
Torchia, M.6
Cohen, F.E.7
Prusiner, S.B.8
-
70
-
-
0022530549
-
Linkage of prion protein and scrapie incubation time genes
-
(1986)
Cell
, vol.46
, pp. 503-511
-
-
Carlson, G.A.1
Kingsbury, D.T.2
Goodman, P.A.3
Coleman, S.4
Marshall, S.T.5
DeArmond, S.6
Westaway, D.7
Prusiner, S.B.8
-
73
-
-
0027275977
-
Neuropathological findings in cattle with clinically suspect but histologically unconfirmed bovine spongiform encephalopathy (BSE)
-
(1993)
J. Comp. Pathol.
, vol.108
, pp. 241-260
-
-
McGill, I.S.1
Wells, G.A.2
-
74
-
-
51849177198
-
Uber eigenartige Erkrankungen des Zentralnervensystems mit bemerkenswertem anatomischem Befunde. (Spastische Pseudosklerose-Encephalomyelpathie mit disseminierten Degenerationsherden)
-
(1921)
Z. ges. Neurol. Psychiatr.
, vol.64
, pp. 147-228
-
-
Jakob, A.1
-
76
-
-
0026542737
-
From slow virus to prion: A review of transmissible spongiform encephalopathies
-
(1992)
Histopathology
, vol.20
, pp. 1-11
-
-
Lantos, P.L.1
-
79
-
-
0342951746
-
A new variant of Creutzfeldt-Jakob disease in the UK
-
(1996)
Lancet
, vol.347
, pp. 921-925
-
-
Will, R.1
Ironside, J.W.2
Zeidler, M.3
Cousens, S.N.4
Estibeiro, K.5
Alperovitch, A.6
Poser, S.7
Pocchiari, M.8
Hofman, A.9
Smith10
-
80
-
-
0024467653
-
Mutations in familial Creutzfeldt-Jakob disease and Gerstmann-Straussler-Scheinker's syndrome
-
(1989)
Exp. Neurol.
, vol.106
, pp. 204-206
-
-
Goldgaber, D.1
Goldfarb, L.G.2
Brown, P.3
Asher, D.M.4
Brown, W.T.5
Lin, S.6
Teener, J.W.7
Feinstone, S.M.8
Rubenstein, R.9
Kascsak, R.J.10
-
81
-
-
0025906297
-
Prion protein mutation in family first reported by Gerstmann, Straussler and Scheinker
-
[letter]
-
(1991)
Lancet
, vol.337
, pp. 1160
-
-
Kretzschmar, H.A.1
Honold, G.2
Seitelberger, F.3
Feucht, M.4
Wessely, P.5
Mehraein, P.6
Budka, H.7
-
82
-
-
0024519771
-
Linkage of a prion protein missense variant to Gerstmann-Straussler syndrome
-
(1989)
Nature
, vol.338
, pp. 342-345
-
-
Hsiao, K.1
Baker, H.F.2
Crow, T.J.3
Poulter, M.4
Owen, F.5
Terwilliger, J.D.6
Westaway, D.7
Ott, J.8
Prusiner, S.B.9
-
85
-
-
0031615941
-
Transmission of spongiform encephalopathy through biological products
-
(1998)
Dev. Biol. Stand.
, vol.93
, pp. 73-78
-
-
Brown, P.1
-
88
-
-
0032488777
-
A transmembrane form of the prion protein in neurodegenerative disease
-
(1998)
Science
, vol.279
, pp. 827-834
-
-
Hegde, R.S.1
Mastrianni, J.A.2
Scott, M.R.3
DeFea, K.A.4
Tremblay, P.5
Torchia, M.6
DeArmond, S.J.7
Prusiner, S.B.8
Lingappa, V.R.9
-
94
-
-
0031444295
-
A crucial role for B cells in neuroinvasive scrapie
-
(1997)
Nature
, vol.390
, pp. 687-690
-
-
Klein, M.A.1
Frigg, R.2
Flechsig, E.3
Raeber, A.J.4
Kalinke, U.5
Bluethmann, H.6
Bootz, F.7
Suter, M.8
Zinkernagel, R.M.9
Aguzzi, A.10
-
97
-
-
0031759918
-
PrP expression in B lymphocytes is not required for prion neuroinvasion
-
(1998)
Nat. Med.
, vol.4
, pp. 1429-1433
-
-
Klein, M.A.1
Frigg, R.2
Raeber, A.J.3
Flechsig, E.4
Hegyi, I.5
Zinkernagel, R.M.6
Weissmann, C.7
Aguzzi, A.8
-
103
-
-
0030684056
-
Astrocyte-specific expression of hamster prion protein (PrP) renders PrP knockout mice susceptible to hamster scrapie
-
(1997)
EMBO J.
, vol.16
, pp. 6057-6065
-
-
Raeber, A.J.1
Race, R.E.2
Brandner, S.3
Priola, S.A.4
Sailer, A.5
Bessen, R.A.6
Mucke, L.7
Manson, J.8
Aguzzi, A.9
Oldstone, M.B.10
Weissmann, C.11
Chesebro, B.12
-
109
-
-
0034650634
-
Reversion of prion protein conformational changes by synthetic beta-sheet breaker peptides
-
(2000)
Lancet
, vol.355
, pp. 192-197
-
-
Soto, C.1
Kascsak, R.J.2
Saborio, G.P.3
Aucouturier, P.4
Wisniewski, T.5
Prelli, F.6
Kascsak, R.7
Mendez, E.8
Harris, D.A.9
Ironside, J.10
Tagliavini, F.11
Carp, R.I.12
Frangione, B.13
-
110
-
-
0028308104
-
[URE3] as an altered URE2 protein: Evidence for a prion analog in Saccharomyces cerevisiae
-
(1994)
Science
, vol.264
, pp. 566-569
-
-
Wickner, R.B.1
|