-
2
-
-
0032923522
-
Molecular genetics of transmissible spongiform encephalopathies
-
Weissmann, C. Molecular genetics of transmissible spongiform encephalopathies. J. Biol Chem. 274, 3-6 (1999).
-
(1999)
J. Biol Chem.
, vol.274
, pp. 3-6
-
-
Weissmann, C.1
-
3
-
-
0032585594
-
Creutzfeldt-Jakob disease and related transmissible spongiform encephalopathies
-
Johnson, R. T. & Gibbs, C. J. Jr Creutzfeldt-Jakob disease and related transmissible spongiform encephalopathies. New Eng. J Med. 399, 1994-2004 (1998).
-
(1998)
New Eng. J Med.
, vol.399
, pp. 1994-2004
-
-
Johnson, R.T.1
Gibbs C.J., Jr.2
-
4
-
-
0030728039
-
Deadly conformations - Protein misfolding in prion disease
-
Horwich, A. L. & Weissman, J. S. Deadly conformations - protein misfolding in prion disease. Cell 89, 499-510 (1997).
-
(1997)
Cell
, vol.89
, pp. 499-510
-
-
Horwich, A.L.1
Weissman, J.S.2
-
5
-
-
0028235176
-
Human spongiform encephalopathy: The national institutes of health series of 300 cases of experimentally transmitted disease
-
Brown, P. et al. Human spongiform encephalopathy: the National Institutes of Health series of 300 cases of experimentally transmitted disease. Ann. Neurol. 35, 513-529 (1994).
-
(1994)
Ann. Neurol.
, vol.35
, pp. 513-529
-
-
Brown, P.1
-
6
-
-
0025119522
-
Immunochemical, molecular genetic, and transmission studies on a case of Gerstmann-Straussler-Scheinker syndrome
-
Tateishi, J. et al. Immunochemical, molecular genetic, and transmission studies on a case of Gerstmann-Straussler-Scheinker syndrome. Neurology 40, 1578-1581 (1990).
-
(1990)
Neurology
, vol.40
, pp. 1578-1581
-
-
Tateishi, J.1
-
7
-
-
0030011971
-
Experimental transmission of Creutzfeldt-Jakob disease and related disorders to rodents
-
Tateishi, J., Kitamoto, T., Hoque, M. Z. & Furukawa, H. Experimental transmission of Creutzfeldt-Jakob disease and related disorders to rodents. Neurology 46, 532-537 (1996).
-
(1996)
Neurology
, vol.46
, pp. 532-537
-
-
Tateishi, J.1
Kitamoto, T.2
Hoque, M.Z.3
Furukawa, H.4
-
8
-
-
0028878943
-
Inherited prion diseases and transmission to rodents
-
Tateishi, J. & Kitamoto, T. Inherited prion diseases and transmission to rodents. Brain Path. 5, 53-59 (1995).
-
(1995)
Brain Path.
, vol.5
, pp. 53-59
-
-
Tateishi, J.1
Kitamoto, T.2
-
9
-
-
0032488777
-
A transmembrane form of the prion protein in neurodegenerative disease
-
Hegde, R. S. et al. A transmembrane form of the prion protein in neurodegenerative disease. Science 279, 827-834 (1998).
-
(1998)
Science
, vol.279
, pp. 827-834
-
-
Hegde, R.S.1
-
10
-
-
0028703452
-
PrP gene dosage determines the timing but not the final intensity or distribution of lesions in scrapie pathology
-
Manson, J. C., Clarke, A. R., McBride, P. A., McConnell, I. & Hope, J. PrP gene dosage determines the timing but not the final intensity or distribution of lesions in scrapie pathology. Neurodegeneration 3, 331-340 (1994).
-
(1994)
Neurodegeneration
, vol.3
, pp. 331-340
-
-
Manson, J.C.1
Clarke, A.R.2
McBride, P.A.3
McConnell, I.4
Hope, J.5
-
11
-
-
0040393220
-
Separation and properties of cellular and scrapie prion proteins
-
Meyer, R. K. et al. Separation and properties of cellular and scrapie prion proteins. Proc. Natl Acad. Sci. USA 83, 2310-2314 (1986).
-
(1986)
Proc. Natl Acad. Sci. USA
, vol.83
, pp. 2310-2314
-
-
Meyer, R.K.1
-
12
-
-
0022487153
-
Pathogenesis of scrapie: Study of the temporal development of clinical symptoms, of infectivity titres and scrapie-associated fibrils in brains of hamsters infected intraperitoneally
-
Czub, M., Braig, H. R. & Diringer, H. Pathogenesis of scrapie: study of the temporal development of clinical symptoms, of infectivity titres and scrapie-associated fibrils in brains of hamsters infected intraperitoneally. J. Gen. Virol. 67, 2005-2009 (1986).
-
(1986)
J. Gen. Virol.
, vol.67
, pp. 2005-2009
-
-
Czub, M.1
Braig, H.R.2
Diringer, H.3
-
13
-
-
0025244011
-
Transgenetic studies implicate interactions between homologous PrP isoforms in scrapie prion replication
-
Prusiner, S. B. Transgenetic studies implicate interactions between homologous PrP isoforms in scrapie prion replication. Cell 63, 673-686 (1990).
-
(1990)
Cell
, vol.63
, pp. 673-686
-
-
Prusiner, S.B.1
-
14
-
-
0014336086
-
Modification of a strain of mouse-adapted scrapie by passage through rats
-
Pattison, I. H. & Jones, K. M. Modification of a strain of mouse-adapted scrapie by passage through rats. Res. Vet. Sci. 9, 408-410 (1968).
-
(1968)
Res. Vet. Sci.
, vol.9
, pp. 408-410
-
-
Pattison, I.H.1
Jones, K.M.2
-
15
-
-
0023499868
-
Mouse polydonal and monoclonal antibody to scrapie-associated fibril proteins
-
Kascsak, R. J. et al Mouse polydonal and monoclonal antibody to scrapie-associated fibril proteins. J. Virol. 61, 3688-3693.
-
J. Virol.
, vol.61
, pp. 3688-3693
-
-
Kascsak, R.J.1
-
16
-
-
0028981199
-
Complete penetrance of Creutzfeldt-Jakob disease in Libyan Jews carrying the E200K mutation in the prion protein gene
-
Spudich, S. et al. Complete penetrance of Creutzfeldt-Jakob disease in Libyan Jews carrying the E200K mutation in the prion protein gene. Mol. Med. 1, 607-613 (1995).
-
(1995)
Mol. Med.
, vol.1
, pp. 607-613
-
-
Spudich, S.1
-
17
-
-
0030069023
-
Insoluble wild-type and protease-resistant mutant prion protein in brains of patients with inherited prion disease
-
Gabizon, R. et al. Insoluble wild-type and protease-resistant mutant prion protein in brains of patients with inherited prion disease. Nature Med. 2, 59-64 (1996).
-
(1996)
Nature Med.
, vol.2
, pp. 59-64
-
-
Gabizon, R.1
-
18
-
-
0026609502
-
Gerstmann-Straussler-Scheinker disease in an Alsation family: Clinical and genetic studies
-
Tranchant, C. et al. Gerstmann-Straussler-Scheinker disease in an Alsation family: clinical and genetic studies. J. Neurol. Neurosurg. Psych. 55, 185-187 (1992).
-
(1992)
J. Neurol. Neurosurg. Psych.
, vol.55
, pp. 185-187
-
-
Tranchant, C.1
-
19
-
-
0032101239
-
The unfolded protein response an intracellular signalling pathway with many surprising features
-
Sidrauski, C., Chapman, R. & Walter, P. The unfolded protein response an intracellular signalling pathway with many surprising features. Trends Cell Biol. 8, 245-249 (1998).
-
(1998)
Trends Cell Biol.
, vol.8
, pp. 245-249
-
-
Sidrauski, C.1
Chapman, R.2
Walter, P.3
-
20
-
-
0029094253
-
Quality control in the secretory pathway
-
Hammond, C. & Helenius, A. Quality control in the secretory pathway. Curr. Opin. Cell Biol. 7, 523-529 (1995).
-
(1995)
Curr. Opin. Cell Biol.
, vol.7
, pp. 523-529
-
-
Hammond, C.1
Helenius, A.2
-
21
-
-
0032113448
-
Regulation of protein topology by trans-acting factors at the endoplasmic reticulum
-
Hegde, R. S., Voigt, S, & Lingappa, V. R. Regulation of protein topology by trans-acting factors at the endoplasmic reticulum. Mol. Cell 2, 85-91 (1998).
-
(1998)
Mol. Cell
, vol.2
, pp. 85-91
-
-
Hegde, R.S.1
Voigt, S.2
Lingappa, V.R.3
-
22
-
-
0025239839
-
Unusual topogenic sequence directs prion protein biogenesis
-
Lopez, C. D., Yost, C. S., Prusiner, S. B., Myers, R. M. & Lingappa, V. R. Unusual topogenic sequence directs prion protein biogenesis. Science 248, 226-229 (1990).
-
(1990)
Science
, vol.248
, pp. 226-229
-
-
Lopez, C.D.1
Yost, C.S.2
Prusiner, S.B.3
Myers, R.M.4
Lingappa, V.R.5
-
23
-
-
0028958208
-
Scrapie prions selectively modify the stress response in neuroblastoma cells
-
Tatzelt, J. et al. Scrapie prions selectively modify the stress response in neuroblastoma cells. Proc. Natl. Acad. Sci. USA 92, 2944-2948 (1995).
-
(1995)
Proc. Natl. Acad. Sci. USA
, vol.92
, pp. 2944-2948
-
-
Tatzelt, J.1
-
24
-
-
0029794668
-
Decreased receptor-mediated calcium response in prion-infected cells correlates with decreased membrane fluidity and IP3 release
-
Wong, K. et al. Decreased receptor-mediated calcium response in prion-infected cells correlates with decreased membrane fluidity and IP3 release. Neurology 47, 741-750 (1996).
-
(1996)
Neurology
, vol.47
, pp. 741-750
-
-
Wong, K.1
-
25
-
-
0031744327
-
Synaptic plasticity in the CA1 area of the hippocampus of scrapie-infected mice
-
Johnston, A. R., Fraser, J. R., Jeffery, M. & MacLeod, N. Synaptic plasticity in the CA1 area of the hippocampus of scrapie-infected mice. Neurobiol. Dis. 5, 188-195 (1998).
-
(1998)
Neurobiol. Dis.
, vol.5
, pp. 188-195
-
-
Johnston, A.R.1
Fraser, J.R.2
Jeffery, M.3
MacLeod, N.4
-
26
-
-
0025103308
-
Rapid detection of Creutzfeldt-Jakob disease and scrapie prion proteins
-
Serban, D., Taraboulous, A., DeArmond, S. J. & Prusiner, S. B, Rapid detection of Creutzfeldt-Jakob disease and scrapie prion proteins. Neurology 40, 110-117 (1990).
-
(1990)
Neurology
, vol.40
, pp. 110-117
-
-
Serban, D.1
Taraboulous, A.2
DeArmond, S.J.3
Prusiner, S.B.4
-
27
-
-
0022529448
-
Monoclonal antibodies to the cellular and scrapie prion protein
-
Barry, R. A. & Prusiner, S. B. Monoclonal antibodies to the cellular and scrapie prion protein. J. Infect. Dis. 154, 518-521 (1986).
-
(1986)
J. Infect. Dis.
, vol.154
, pp. 518-521
-
-
Barry, R.A.1
Prusiner, S.B.2
-
28
-
-
0029740354
-
Interactions between wild-type and mutant prion proteins modulate neurode-generation in transgenic mice
-
Telling, G. C. et al. Interactions between wild-type and mutant prion proteins modulate neurode-generation in transgenic mice. Genes Dev. 10, 1736-1750 (1996).
-
(1996)
Genes Dev.
, vol.10
, pp. 1736-1750
-
-
Telling, G.C.1
-
29
-
-
0016469066
-
Comparison of scrapie and transmissible mink encephalopathy in hamsters. II. Clinical signs, pathology, and pathogenesis
-
Marsh, R. F. & Kimberlin, R. H. Comparison of scrapie and transmissible mink encephalopathy in hamsters. II. Clinical signs, pathology, and pathogenesis. J. Infect. Dis. 131, 104-110 (1975).
-
(1975)
J. Infect. Dis.
, vol.131
, pp. 104-110
-
-
Marsh, R.F.1
Kimberlin, R.H.2
-
30
-
-
49749206702
-
Encephalopathy in mice produced by inoculation with scrapie brain material
-
Chandler, R. L. Encephalopathy in mice produced by inoculation with scrapie brain material. Lancet 1, 1378-1379 (1961).
-
(1961)
Lancet
, vol.1
, pp. 1378-1379
-
-
Chandler, R.L.1
|