Neurodegeneration in a Drosophila model of adrenoleukodystrophy: The roles of the Bubblegum and Double bubble acyl-CoA synthetases

DMM Disease Models and Mechanisms

Volumn 9, Issue 4, 2016, Pages 377-387

  Sivachenko, Anna ^a   Gordon, Hannah B ^a   Kimball, Suzanne S ^a   Gavin, Erin J ^a   Bonkowsky, Joshua L ^a   Letsou, Anthea ^a  

^a UNIVERSITY OF UTAH SCHOOL OF MEDICINE   (United States)

Author keywords

Acyl CoA synthetase; Bubblegum; Double bubble; Drosophila; Neurodegeneration; SLC27a6; VLCFA

Indexed keywords

ABC TRANSPORTER; LONG CHAIN FATTY ACID COENZYME A LIGASE; BGM PROTEIN, DROSOPHILA; COENZYME A LIGASE; DOUBLE BUBBLE PROTEIN, DROSOPHILA; DROSOPHILA PROTEIN; LIPID;

ADRENOLEUKODYSTROPHY; ARTICLE; CENTRAL NERVOUS SYSTEM; DROSOPHILA MELANOGASTER; ELECTRON MICROSCOPY; ENZYME ACTIVITY; FATTY ACID METABOLISM; FRUIT FLY MODEL; GENE FUNCTION; GENE MUTATION; GENE SILENCING; NERVE DEGENERATION; NONHUMAN; PHENOTYPE; PIGMENT CELL; PRIORITY JOURNAL; PROTEIN FUNCTION; ANIMAL; CELL DEATH; CELL MEMBRANE; CHEMISTRY; CYTOLOGY; DISEASE MODEL; ENZYMOLOGY; GENE DUPLICATION; GENE KNOCKOUT; GENETICS; HUMAN; METABOLISM; MUTATION; NUCLEOTIDE SEQUENCE; PATHOLOGY; ULTRASTRUCTURE;

ADRENOLEUKODYSTROPHY; ANIMALS; BASE SEQUENCE; CELL DEATH; CELL MEMBRANE; CENTRAL NERVOUS SYSTEM; COENZYME A LIGASES; DISEASE MODELS, ANIMAL; DROSOPHILA MELANOGASTER; DROSOPHILA PROTEINS; GENE DUPLICATION; GENE KNOCKOUT TECHNIQUES; HUMANS; LIPIDS; MUTATION; NERVE DEGENERATION; PHENOTYPE;

EID: 84963650464     PISSN: 17548403     EISSN: 17548411     Source Type: Journal    
DOI: 10.1242/dmm.022244     Document Type: Article

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