Localization of nervonic acid β-oxidation in human and rodent peroxisomes: Impaired oxidation in Zellweger syndrome and X-linked adrenoleukodystrophy

Journal of Lipid Research

Volumn 39, Issue 11, 1998, Pages 2161-2171

  Sandhir, Rajat ^a   Khan, Mushfiquddin ^a   Chahal, Amarjit ^a   Singh, Inderjit ^a  

^a MEDICAL UNIVERSITY OF SOUTH CAROLINA   (United States)

Author keywords

Nervonic acid; Peroxisome; Very long chain fatty acids; X linked adrenoleukodystrophy; Zellweger syndrome

Indexed keywords

15 TETRACOSENOIC ACID; 2,4 DIENOYL COENZYME A REDUCTASE (NADPH); ETOMOXIR; LIGNOCERIC ACID; LONG CHAIN FATTY ACID COENZYME A LIGASE; LORENZO OIL; PALMITIC ACID; PHYTANIC ACID; UNCLASSIFIED DRUG; VERY LONG CHAIN FATTY ACID;

ADRENOLEUKODYSTROPHY; ARTICLE; BIOACCUMULATION; CONTROLLED STUDY; DIAGNOSTIC VALUE; DIET THERAPY; ENZYME ACTIVITY; ENZYME REPRESSION; FATTY ACID BLOOD LEVEL; FATTY ACID OXIDATION; FIBROBLAST; GENETIC TRANSFECTION; HUMAN; HUMAN CELL; IMMUNOFLUORESCENCE; IMMUNOPRECIPITATION; LIPID COMPOSITION; PEROXISOME; PRIORITY JOURNAL; REACTION TIME; TISSUE DISTRIBUTION; X CHROMOSOME LINKED DISORDER; ZELLWEGER SYNDROME;

ADRENOLEUKODYSTROPHY; ANIMALS; CELL LINE; COENZYME A LIGASES; FATTY ACIDS; FATTY ACIDS, MONOUNSATURATED; FIBROBLASTS; HUMANS; LINKAGE (GENETICS); MICROBODIES; NEUROGLIA; OXIDATION-REDUCTION; RATS; RATS, SPRAGUE-DAWLEY; REPRESSOR PROTEINS; SACCHAROMYCES CEREVISIAE PROTEINS; X CHROMOSOME; ZELLWEGER SYNDROME;

EID: 0031723632     PISSN: 00222275     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

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