A very long-chain acyl-CoA synthetase-deficient mouse and its relevance to X-linked adrenoleukodystrophy

Human Molecular Genetics

Volumn 12, Issue 10, 2003, Pages 1145-1154

  Heinzer, Ann K ^a   Watkins, Paul A ^a   Lu, Jyh Feng ^b   Kemp, Stephan ^c   Moser, Ann B ^a   Li, Yuan Yuan ^a   Mihalik, Stephanie ^a   Powers, James M ^d   Smith, Kirby D ^a  

^a JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b FU JEN CATHOLIC UNIVERSITY   (Taiwan)

^c UNIVERSITY OF AMSTERDAM   (Netherlands)

^d UNIVERSITY OF ROCHESTER MEDICAL CENTER   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

LONG CHAIN FATTY ACID COENZYME A LIGASE; MEMBRANE PROTEIN; VERY LONG CHAIN FATTY ACID;

ADRENOLEUKODYSTROPHY; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CONTROLLED STUDY; DISEASE ASSOCIATION; DISEASE SEVERITY; ENZYME ACTIVITY; ENZYME DEFICIENCY; FATTY ACID OXIDATION; FEMALE; GENE MUTATION; KNOCKOUT MOUSE; MALE; MOUSE; NONHUMAN; PEROXISOME; PHENOTYPE; PRIORITY JOURNAL; PROTEIN PROTEIN INTERACTION; X CHROMOSOME LINKED DISORDER;

ADRENOLEUKODYSTROPHY; ANIMALS; ATP-BINDING CASSETTE TRANSPORTERS; BRAIN; COENZYME A LIGASES; FATTY ACIDS; HUMANS; KIDNEY; LIVER; MICE; MICE, KNOCKOUT; REPRESSOR PROTEINS; SACCHAROMYCES CEREVISIAE PROTEINS;

ANIMALIA;

EID: 0038778368     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/ddg126     Document Type: Article

References (41)

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