Circadian profiling in two mouse models of lysosomal storage disorders; Niemann Pick type-C and Sandhoff disease

Behavioural Brain Research

Volumn 297, Issue , 2016, Pages 213-223

  Richardson, Katie ^a   Livieratos, Achilleas ^a   Dumbill, Richard ^a   Hughes, Steven ^a   Ang, Gauri ^a   Smith, David A ^a   Morris, Lauren ^a   Brown, Laurence A ^a   Peirson, Stuart N ^a   Platt, Frances M ^a   Davies, Kay E ^a   Oliver, Peter L ^a  

^a UNIVERSITY OF OXFORD   (United Kingdom)

Author keywords

Ataxia; Circadian; Lysosome storage disorder; Mouse mutant

Indexed keywords

PER1 PROTEIN; BETA N ACETYLHEXOSAMINIDASE; CHOLESTEROL; CLOCK PROTEIN, MOUSE; MELANOPSIN; NPC1 PROTEIN, MOUSE; POU4F1 PROTEIN, MOUSE; PROTEIN; SCOTOPSIN; TRANSCRIPTION FACTOR CLOCK; TRANSCRIPTION FACTOR POU4F1;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BEHAVIOR CHANGE; CIRCADIAN RHYTHM; CONTROLLED STUDY; GENE; GENE EXPRESSION; GENETIC ANALYSIS; LIGHT DARK CYCLE; LIPID STORAGE; MOLECULAR CLOCK; MOUSE; NEUROPATHOLOGY; NIEMANN PICK DISEASE; NONHUMAN; PER1 GENE; PHENOTYPE; PRIORITY JOURNAL; SANDHOFF DISEASE; SUPRACHIASMATIC NUCLEUS; ACTIMETRY; ANIMAL; BAGG ALBINO MOUSE; COMPARATIVE STUDY; DISEASE MODEL; FLUORESCENT ANTIBODY TECHNIQUE; GENETICS; KNOCKOUT MOUSE; METABOLISM; MOTOR ACTIVITY; PATHOLOGY; PATHOPHYSIOLOGY; PHOTOPERIODICITY; PHYSIOLOGY; RETINA;

ACTIGRAPHY; ANIMALS; BETA-N-ACETYLHEXOSAMINIDASES; CHOLESTEROL; CIRCADIAN RHYTHM; CLOCK PROTEINS; DISEASE MODELS, ANIMAL; FLUORESCENT ANTIBODY TECHNIQUE; MICE, INBRED BALB C; MICE, KNOCKOUT; MOTOR ACTIVITY; NIEMANN-PICK DISEASE, TYPE C; PHOTOPERIOD; PROTEINS; RETINA; ROD OPSINS; SANDHOFF DISEASE; SUPRACHIASMATIC NUCLEUS; TRANSCRIPTION FACTOR BRN-3A;

EID: 84944937637     PISSN: 01664328     EISSN: 18727549     Source Type: Journal    
DOI: 10.1016/j.bbr.2015.10.021     Document Type: Article

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