Ultrastructural studies of ALS mitochondria connect altered function and permeability with defects of mitophagy and mitochondriogenesis

Frontiers in Cellular Neuroscience

Volumn 9, Issue september, 2015, Pages

  Ruffoli, Riccardo ^a   Bartalucci, Alessia ^a   Frati, Alessandro ^b   Fornai, Francesco ^a,b  

^a UNIVERSITY OF PISA   (Italy)

^b IRCCS NEUROMED   (Italy)

Author keywords

Amyotrophic lateral sclerosis; Autophagy; Biogenesis of mitochondria; Electron microscopy; Human patients; Mitochondria; Motor neuron

Indexed keywords

CALCIUM CHANNEL; COPPER ZINC SUPEROXIDE DISMUTASE; CYCLOPHILIN D; DYNACTIN; DYNEIN ADENOSINE TRIPHOSPHATASE; ESCRT PROTEIN; LITHIUM; OPTINEURIN; PROTEIN P62; RAB PROTEIN; TAR DNA BINDING PROTEIN; UBIQUITIN; VALOSIN CONTAINING PROTEIN; VALPROIC ACID;

AMYOTROPHIC LATERAL SCLEROSIS; AUTOPHAGOSOME; AUTOPHAGY; CALCIUM HOMEOSTASIS; CELL DAMAGE; CELL FUNCTION; CELLULAR, SUBCELLULAR AND MOLECULAR BIOLOGICAL PHENOMENA AND FUNCTIONS; CHROMOSOME 9; HUMAN; MITOCHONDRIOGENESIS; MITOCHONDRION; MITOPHAGY; MOTONEURON; MULTIPHOTON MICROSCOPY; MUTATION; NERVE FIBER; NONHUMAN; OPEN READING FRAME; PERIKARYON; POLYMERASE CHAIN REACTION; REVIEW; ULTRASTRUCTURE;

EID: 84941009269     PISSN: 16625102     EISSN: None     Source Type: Journal    
DOI: 10.3389/fncel.2015.00341     Document Type: Review

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