Stem cell-derived motor neurons from spinal and bulbar muscular atrophy patients

Neurobiology of Disease

Volumn 70, Issue , 2014, Pages 12-20

  Grunseich, Christopher ^a   Zukosky, Kristen ^a   Kats, Ilona R ^a   Ghosh, Laboni ^a   Harmison, George G ^a   Bott, Laura C ^a,b   Rinaldi, Carlo ^a   Chen, Ke lian ^a   Chen, Guibin ^c   Boehm, Manfred ^c   Fischbeck, Kenneth H ^a  

^a NATIONAL INSTITUTE OF NEUROLOGICAL DISORDERS AND STROKE   (United States)

^b KAROLINSKA INSTITUTE   (Sweden)

^c NATIONAL HEART LUNG AND BLOOD INSTITUTE   (United States)

Author keywords

Androgen receptor; Induced pluripotent stem cells; Motor neuron disease; Spinal and bulbar muscular atrophy

Indexed keywords

ANDROGEN RECEPTOR; BIOLOGICAL MARKER; PROTEIN CHAT; PROTEIN HB9; PROTEIN ISL1; PROTEIN SMI 32; UNCLASSIFIED DRUG; ALPHA TUBULIN; CELL PROTEIN; CHAT PROTEIN; HB9 PROTEIN; HISTONE DEACETYLASE 6; ISL1 PROTEIN; LYSOSOME ASSOCIATED MEMBRANE PROTEIN 1; SMI 32 PROTEIN; HDAC6 PROTEIN, HUMAN; HISTONE DEACETYLASE; REPETITIVE DNA; TUBULIN;

ADULT; AGED; ARTICLE; CAG REPEAT; CELL CLONE; CELL EXPANSION; CLINICAL ARTICLE; CONTROLLED STUDY; FEMALE; FIBROBLAST; HUMAN; HUMAN CELL; HUMAN TISSUE; IMMUNOREACTIVITY; KENNEDY DISEASE; MALE; MOTONEURON; NERVE CELL DIFFERENTIATION; NEURAL STEM CELL; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN STABILITY; PROTEIN TRANSPORT; CELL COMPARTMENTALIZATION; CELL DIFFERENTIATION; CELL SURVIVAL; CELLULAR DISTRIBUTION; ENRICHMENT CULTURE; ENZYME ACTIVITY; LYSOSOME; MIDDLE AGED; PLURIPOTENT STEM CELL; PROTEIN ACETYLATION; PROTEIN GLYCOSYLATION; PROTEIN LOCALIZATION; SPINAL CORD; YOUNG ADULT; ACETYLATION; CELL CULTURE; DEFICIENCY; GENETICS; METABOLISM; NERVOUS SYSTEM DEVELOPMENT; PATHOPHYSIOLOGY; PHYSIOLOGY;

ACETYLATION; ADULT; AGED; BULBO-SPINAL ATROPHY, X-LINKED; CELLS, CULTURED; DNA REPEAT EXPANSION; FEMALE; FIBROBLASTS; HISTONE DEACETYLASES; HUMANS; INDUCED PLURIPOTENT STEM CELLS; MALE; MIDDLE AGED; MOTOR NEURONS; NEUROGENESIS; RECEPTORS, ANDROGEN; TUBULIN; YOUNG ADULT;

EID: 84903373763     PISSN: 09699961     EISSN: 1095953X     Source Type: Journal    
DOI: 10.1016/j.nbd.2014.05.038     Document Type: Article

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