Natural history of spinal and bulbar muscular atrophy (SBMA): A study of 223 Japanese patients

Brain

Volumn 129, Issue 6, 2006, Pages 1446-1455

  Atsuta, Naoki ^a   Watanabe, Hirohisa ^a   Ito, Mizuki ^a   Banno, Haruhiko ^a   Suzuki, Keisuke ^a   Katsuno, Masahisa ^a   Tanaka, Fumiaki ^a   Tamakoshi, Akiko ^a   Sobue, Gen ^a  

^a NAGOYA UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

Author keywords

ADL milestone; Kennedy disease; Motoneuron disease; Natural history; SBMA

Indexed keywords

ANDROGEN RECEPTOR; POLYGLUTAMINE; TESTOSTERONE;

ADULT; AGED; ARTICLE; DAILY LIFE ACTIVITY; DISEASE COURSE; DYSARTHRIA; DYSPHAGIA; GENETIC ANALYSIS; HAND TREMOR; HUMAN; KENNEDY DISEASE; MAJOR CLINICAL STUDY; MOTOR NEURON DISEASE; MUSCLE WEAKNESS; NERVE DEGENERATION; PNEUMONIA; PRIORITY JOURNAL; RESPIRATORY FAILURE; TESTOSTERONE BLOOD LEVEL; WALKING AID; WHEELCHAIR; AGE DISTRIBUTION; CAUSE OF DEATH; DISABILITY; FOLLOW UP; GENETICS; MALE; MIDDLE AGED; ONSET AGE; PATHOPHYSIOLOGY; PROGNOSIS; SPINAL MUSCULAR ATROPHY; TREMOR; TRINUCLEOTIDE REPEAT;

ACTIVITIES OF DAILY LIVING; ADULT; AGE DISTRIBUTION; AGE OF ONSET; AGED; AGED, 80 AND OVER; CAUSE OF DEATH; DISABILITY EVALUATION; DISEASE PROGRESSION; FOLLOW-UP STUDIES; HUMANS; MALE; MIDDLE AGED; MUSCLE WEAKNESS; MUSCULAR ATROPHY, SPINAL; PROGNOSIS; RECEPTORS, ANDROGEN; TREMOR; TRINUCLEOTIDE REPEATS;

EID: 33745115069     PISSN: 00068950     EISSN: 14602156     Source Type: Journal    
DOI: 10.1093/brain/awl096     Document Type: Article

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