A re-evaluation of life-long severe galactose restriction for the nutrition management of classic galactosemia

Molecular Genetics and Metabolism

Volumn 112, Issue 3, 2014, Pages 191-197

  Van Calcar, Sandra C ^a   Bernstein, Laurie E ^b   Rohr, Frances J ^c   Scaman, Christine H ^d   Yannicelli, Steven ^e   Berry, Gerard T ^c  

^a UNIVERSITY OF WISCONSIN SCHOOL OF MEDICINE AND PUBLIC HEALTH   (United States)

^b UNIVERSITY OF COLORADO SCHOOL OF MEDICINE   (United States)

^c BOSTON CHILDREN S HOSPITAL   (United States)

^d UNIVERSITY OF BRITISH COLUMBIA   (Canada)

^e MEDIMMUNE   (United States)

Author keywords

Diet treatment; Galactose restriction; Galactose 1 phosphate uridyltransferase deficiency; Inborn errors of metabolism; Lactose

Indexed keywords

GALACTOSE;

CHEESE; DIET RESTRICTION; DIET THERAPY; FOOD; FRUIT; GALACTOSEMIA; HUMAN; LEGUME; OUTCOMES RESEARCH; PRIORITY JOURNAL; REVIEW; VEGETABLE; AGE; LOW CARBOHYDRATE DIET; META ANALYSIS;

AGE FACTORS; DIET, CARBOHYDRATE-RESTRICTED; FOOD; GALACTOSE; GALACTOSEMIAS; HUMANS;

EID: 84902540273     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2014.04.004     Document Type: Review

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