GALT deficiency causes UDP-hexose deficit in human galactosemic cells

Glycobiology

Volumn 13, Issue 4, 2003, Pages 285-294

  Lai, K ^a,b   Langley, S D ^a   Khwaja, F W ^a   Schmitt, E W ^a   Elsas, L J ^a  

^a EMORY UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY OF MIAMI MILLER SCHOOL OF MEDICINE   (United States)

Author keywords

Competitive inhibition; Fibroblast; Galactose 1 phosphate uridyltransferase; Galactosemia; UDP glucose pyrophosphorylase

Indexed keywords

AGGLUTININ; GALACTOSE 1 PHOSPHATE URIDYLYLTRANSFERASE; GLYCOPROTEIN; HEXOSE; N ACETYLGLUCOSAMINE; URIDINE DIPHOSPHATE; URIDINE TRIPHOSPHATE GLUCOSE 1 PHOSPHATE URIDYLYLTRANSFERASE;

ARTICLE; CARBOHYDRATE METABOLISM; CELL TRANSFORMATION; CONTROLLED STUDY; ENZYME INHIBITION; ENZYME KINETICS; ENZYME MECHANISM; FIBROBLAST; GALACTOSEMIA; GENETIC TRANSFECTION; HUMAN; HUMAN CELL; PRIORITY JOURNAL; PROTEIN BINDING; PROTEIN GLYCOSYLATION; PROTEIN ISOLATION; SAMBUCUS NIGRA;

CELL LINE, TRANSFORMED; CELL TRANSFORMATION, VIRAL; CELLS, CULTURED; FIBROBLASTS; GALACTOSE; GALACTOSEPHOSPHATES; GLYCOSYLATION; HUMANS; KINETICS; PHENOTYPE; SIMIAN VIRUS 40; TRANSFECTION; URIDINE DIPHOSPHATE GLUCOSE; UTP-GLUCOSE-1-PHOSPHATE URIDYLYLTRANSFERASE; UTP-HEXOSE-1-PHOSPHATE URIDYLYLTRANSFERASE;

SAMBUCUS NIGRA;

EID: 0037718404     PISSN: 09596658     EISSN: None     Source Type: Journal    
DOI: 10.1093/glycob/cwg033     Document Type: Article

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