Ciliopathy proteins regulate paracrine signaling by modulating proteasomal degradation of mediators

Journal of Clinical Investigation

Volumn 124, Issue 5, 2014, Pages 2059-2070

  Liu, Yangfan P ^a   Tsai, I Chun ^a   Morleo, Manuela ^b   Oh, Edwin C ^a   Leitch, Carmen C ^c   Massa, Filomena ^b   Lee, Byung Hoon ^d   Parker, David S ^a   Finley, Daniel ^d   Zaghloul, Norann A ^c   Franco, Brunella ^b,e   Katsanis, Nicholas ^a  

^a DUKE UNIVERSITY MEDICAL CENTER   (United States)

^b TELETHON INSTITUTE OF GENETICS AND MEDICINE TIGEM   (Italy)

^c UNIVERSITY OF MARYLAND SCHOOL OF MEDICINE   (United States)

^d HARVARD MEDICAL SCHOOL   (United States)

^e UNIVERSITY OF NAPLES FEDERICO II   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

BARDET BIEDL SYNDROME 4 PROTEIN; CELL PROTEIN; I KAPPA B BETA; IMMUNOGLOBULIN ENHANCER BINDING PROTEIN; MEVALONOLACTONE; ORALFACIAL DIGITAL SYNDROME 1 PROTEIN; PROTEASOME; SULFORAPHANE; UNCLASSIFIED DRUG;

ANIMAL CELL CULTURE; ANIMAL EXPERIMENT; ANIMAL TISSUE; ARTICLE; EUKARYOTIC FLAGELLUM; IMMUNOBLOTTING; MOUSE; NONHUMAN; PARACRINE SIGNALING; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN DEPLETION; PROTEIN EXPRESSION; PROTEIN INTERACTION; REGULATORY MECHANISM; ZEBRA FISH;

ANIMALS; ANTICARCINOGENIC AGENTS; CELL LINE; CILIARY MOTILITY DISORDERS; HUMANS; I-KAPPA B PROTEINS; ISOTHIOCYANATES; MEVALONIC ACID; MICE; MICROTUBULE-ASSOCIATED PROTEINS; PROTEASOME ENDOPEPTIDASE COMPLEX; PROTEINS; PROTEOLYSIS; ZEBRAFISH; ZEBRAFISH PROTEINS;

EID: 84899758669     PISSN: 00219738     EISSN: 15588238     Source Type: Journal    
DOI: 10.1172/JCI71898     Document Type: Article

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