Dysregulated interactions between lamin A and SUN1 induce abnormalities in the nuclear envelope and endoplasmic reticulum in progeric laminopathies

Journal of Cell Science

Volumn 127, Issue 8, 2014, Pages 1792-1804

  Chen, Zi Jie ^a   Wang, Wan Ping ^a   Chen, Yu Ching ^a   Wang, Jing Ya ^a   Lin, Wen Hsin ^a   Tai, Lin Ai ^a   Liou, Gan Guang ^a   Yang, Chung Shi ^a   Chi, Ya Hui ^a,b  

^a NATIONAL HEALTH RESEARCH INSTITUTES   (Taiwan)

^b CHINA MEDICAL UNIVERSITY   (Taiwan)

Author keywords

HGPS; Lamin A; Nuclear envelope; Progeria; SUN1

Indexed keywords

CYSTEINE; LAMIN A; PROTEIN; SUN1 PROTEIN; UNCLASSIFIED DRUG; MEMBRANE PROTEIN; MICROTUBULE ASSOCIATED PROTEIN; NUCLEAR PROTEIN; PRELAMIN A; PROTEIN PRECURSOR; SUN1 PROTEIN, HUMAN;

ARTICLE; CELL CYCLE PROGRESSION; CELL DIVISION; CELL NUCLEUS MEMBRANE; CELL STRUCTURE; CONTROLLED STUDY; DISEASE COURSE; ELECTRON MICROSCOPY; ENDOPLASMIC RETICULUM; FARNESYLATION; GOLGI COMPLEX; HUMAN; HUMAN CELL; LAMINOPATHY; MITOSIS; PHENOTYPE; PRIORITY JOURNAL; PROGERIA; PROTEIN AGGREGATION; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN INTERACTION; PROTEIN MODIFICATION; PROTEIN MOTIF; FIBROBLAST; GENETICS; HELA CELL LINE; METABOLISM; PATHOLOGY; POINT MUTATION; PRENYLATION; PROTEIN PROCESSING; PROTEIN TRANSPORT; SKIN;

ENDOPLASMIC RETICULUM; FIBROBLASTS; HELA CELLS; HUMANS; LAMIN TYPE A; MEMBRANE PROTEINS; MICROTUBULE-ASSOCIATED PROTEINS; MITOSIS; NUCLEAR ENVELOPE; NUCLEAR PROTEINS; POINT MUTATION; PRENYLATION; PROGERIA; PROTEIN PRECURSORS; PROTEIN PROCESSING, POST-TRANSLATIONAL; PROTEIN TRANSPORT; SKIN;

EID: 84898887269     PISSN: 00219533     EISSN: 14779137     Source Type: Journal    
DOI: 10.1242/jcs.139683     Document Type: Article

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