Accumulation of the inner nuclear envelope protein Sun1 is pathogenic in progeric and dystrophic laminopathies

Cell

Volumn 149, Issue 3, 2012, Pages 565-577

  Chen, Chia Yen ^a   Chi, Ya Hui ^d   Mutalif, Rafidah Abdul ^e   Starost, Matthew F ^b   Myers, Timothy G ^a   Anderson, Stasia A ^c   Stewart, Colin L ^e,f   Jeang, Kuan Teh ^a  

^a NATIONAL INSTITUTE OF ALLERGY AND INFECTIOUS DISEASES   (United States)

^b NATIONAL INSTITUTES OF HEALTH   (United States)

^c NATIONAL HEART LUNG AND BLOOD INSTITUTE   (United States)

^d NATIONAL HEALTH RESEARCH INSTITUTES   (Taiwan)

^e INSTITUTE OF MEDICAL BIOLOGY   (Singapore)

^f NATIONAL UNIVERSITY OF SINGAPORE   (Singapore)

Author keywords

[No Author keywords available]

Indexed keywords

MEMBRANE PROTEIN; PROTEIN SUN1; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; EMERY DREIFUSS MUSCULAR DYSTROPHY; FIBROBLAST; GENE; GENE MUTATION; LIFESPAN; LMNA GENE; LONGEVITY; MOUSE; NONHUMAN; PATHOGENICITY; PRIORITY JOURNAL; PROGERIA;

ANIMALIA; MUS;

EID: 84860327128     PISSN: 00928674     EISSN: 10974172     Source Type: Journal    
DOI: 10.1016/j.cell.2012.01.059     Document Type: Article

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