Long-chain Acyl-CoA dehydrogenase deficiency as a cause of pulmonary surfactant dysfunction

Journal of Biological Chemistry

Volumn 289, Issue 15, 2014, Pages 10668-10679

  Goetzman, Eric S ^a,b   Alcorn, John F ^a   Bharathi, Sivakama S ^a   Uppala, Radha ^a   McHugh, Kevin J ^a   Kosmider, Beata ^c   Chen, Rimei ^d   Zuo, Yi Y ^d   Beck, Megan E ^c   McKinney, Richard W ^a   Skilling, Helen ^a   Suhrie, Kristen R ^a   Karunanidhi, Anuradha ^a   Yeasted, Renita ^a   Otsubo, Chikara ^a   Ellis, Bryon ^a   Tyurina, Yulia Y ^e,f   Kagan, Valerian E ^e,f   Mallampalli, Rama K ^a,g   Vockley, Jerry ^a,b  

^a UNIVERSITY OF PITTSBURGH SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY OF PITTSBURGH GRADUATE SCHOOL OF PUBLIC HEALTH   (United States)

^c DEPARTMENT OF MEDICINE   (United States)

^d University of Hawaii at Manoa   (United States)

^e Center for Free Radical and Antioxidant Health   (United States)

^f UNIVERSITY OF PITTSBURGH   (United States)

^g VETERANS AFFAIRS MEDICAL CENTER   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

AMINO ACIDS; BIOLOGICAL ORGANS; CHAINS; FATTY ACIDS; MAMMALS; OXIDATION; PATHOLOGY; SURFACE ACTIVE AGENTS;

COMPRESSION-EXPANSION; EPITHELIAL PERMEABILITY; FATTY ACID OXIDATION; HISTOLOGICAL EXAMINATION; LONG-CHAIN ACYL-COA; PHOSPHATIDYLGLYCEROLS; PHYSIOLOGICAL ROLES; PULMONARY SURFACTANTS;

PHOSPHOLIPIDS;

LONG CHAIN ACYL COENZYME A DEHYDROGENASE; LUNG SURFACTANT; PHOSPHATIDYLCHOLINE; PHOSPHATIDYLGLYCEROL; PHOSPHOLIPID; SERUM ALBUMIN;

ALBUMIN BLOOD LEVEL; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL MEMBRANE PERMEABILITY; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; ENERGY METABOLISM; ENZYME ANALYSIS; ENZYME DEFICIENCY; ENZYME LOCALIZATION; ENZYME SYNTHESIS; FATTY ACID METABOLISM; FATTY ACID OXIDATION; HISTOLOGY; HUMAN; HUMAN CELL; HUMAN TISSUE; INFANT; LUNG ALVEOLUS CELL TYPE 2; LUNG ALVEOLUS EPITHELIUM; LUNG COMPLIANCE; LUNG DISEASE; LUNG FUNCTION; LUNG LAVAGE; LUNG MECHANICS; LUNG PARENCHYMA; MOUSE; NONHUMAN; PHOSPHOLIPID SYNTHESIS; PRIORITY JOURNAL; PROTEIN EXPRESSION; PULMONARY SURFACTANT DYSFUNCTION; SIGNAL TRANSDUCTION;

ACYL-COA DEHYDROGENASE; FATTY ACID OXIDATION; GENETIC DISEASES; LUNG; MITOCHONDRIAL METABOLISM; PULMONARY SURFACTANT;

ACYL-COA DEHYDROGENASE, LONG-CHAIN; ADULT; ANIMALS; BRONCHI; CELL LINE, TUMOR; COENZYME A; DISEASE MODELS, ANIMAL; EPITHELIAL CELLS; FATTY ACIDS; FEMALE; HOMOZYGOTE; HUMANS; INFANT; INFANT, NEWBORN; LIPID METABOLISM, INBORN ERRORS; LUNG; LUNG DISEASES; LUNG NEOPLASMS; MALE; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; OXYGEN; PHOSPHATIDYLCHOLINES; PHOSPHATIDYLGLYCEROLS; POLYMORPHISM, GENETIC; PULMONARY ALVEOLI; PULMONARY SURFACTANTS;

EID: 84898657934     PISSN: 00219258     EISSN: 1083351X     Source Type: Journal    
DOI: 10.1074/jbc.M113.540260     Document Type: Article

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