Netherton syndrome: Skin inflammation and allergy by loss of protease inhibition

Cell and Tissue Research

Volumn 351, Issue 2, 2013, Pages 289-300

  Hovnanian, Alain ^a,b,c  

^a INSERM   (France)

^b IMAGINE INSTITUTE   (France)

^c UNIVERSITÉ PARIS DESCARTES   (France)

Author keywords

Kallikreins (KLK); Lympho epithelial Kazal type related inhibitor type 5 (LEKTI); Protease activated receptor 2 (PAR 2); Serine protease inhibitor of kazal type 5 (SPINK5); Thymic stromal lymphopoietin (TSLP)

Indexed keywords

ELASTASE; ELASTASE II; IMMUNOGLOBULIN; INTERLEUKIN 1BETA CONVERTING ENZYME; KALLIKREIN 5; PROTEINASE; PROTEINASE ACTIVATED RECEPTOR 2; STRATUM CORNEUM CHYMOTRYPTIC ENZYME; THYMIC STROMAL LYMPHOPOIETIN; THYMUS AND ACTIVATION REGULATED CHEMOKINE; TUMOR NECROSIS FACTOR ALPHA; TUMOR NECROSIS FACTOR ALPHA INHIBITOR; UNCLASSIFIED DRUG; LEUKOCYTE ELASTASE INHIBITOR; PEPTIDE HYDROLASE; SPINK5 PROTEIN, HUMAN;

ADULTHOOD; ATOPIC DERMATITIS; CLINICAL FEATURE; DERMATITIS; DISEASE ASSOCIATION; DRUG EFFECT; ENZYME ACTIVATION; ENZYME ACTIVITY; ENZYME INHIBITION; EXPERIMENTAL MODEL; GENETIC CODE; GENOTYPE PHENOTYPE CORRELATION; HUMAN; IMMUNOPATHOLOGY; LOSS OF FUNCTION MUTATION; MUTATOR GENE; NETHERTON DISEASE; NONHUMAN; PATHOPHYSIOLOGY; PRIORITY JOURNAL; PROTEIN EXPRESSION; REVIEW; SIGNAL TRANSDUCTION; SITE DIRECTED MUTAGENESIS; SKIN ALLERGY; SPINK5 GENE; STRATUM CORNEUM; TREATMENT PLANNING; ANIMAL; DEFICIENCY; ENZYMOLOGY; GENETICS; HYPERSENSITIVITY; IMMUNOLOGY; METABOLISM; PATHOLOGY;

MURINAE;

ANIMALS; DERMATITIS; HUMANS; HYPERSENSITIVITY; NETHERTON SYNDROME; PEPTIDE HYDROLASES; PROTEINASE INHIBITORY PROTEINS, SECRETORY;

EID: 84891415326     PISSN: 0302766X     EISSN: 14320878     Source Type: Journal    
DOI: 10.1007/s00441-013-1558-1     Document Type: Review

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