Selective antibody deficiency to bacterial polysaccharide antigens in patients with Netherton syndrome

Pediatric Dermatology

Volumn 16, Issue 1, 1999, Pages 19-22

  Stryk, Steve ^a   Siegfried, Elaine C ^b   Knutsen, Alan P ^a  

^a SAINT LOUIS UNIVERSITY   (United States)

^b SAINT LOUIS UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

BACTERIAL POLYSACCHARIDE; BACTERIUM ANTIBODY; IMMUNOGLOBULIN A; IMMUNOGLOBULIN G2; PROTEIN ANTIBODY;

ARTICLE; AUTOSOMAL RECESSIVE DISORDER; CASE REPORT; FEMALE; HUMAN; HUMORAL IMMUNE DEFICIENCY; INFANT; LUNG INFECTION; MALE; PRIORITY JOURNAL; RECURRENT INFECTION; SINUSITIS; SKIN DISEASE; SKIN INFECTION;

ANTIGENS, BACTERIAL; FEMALE; HAIR DISEASES; HUMANS; ICHTHYOSIS; IGA DEFICIENCY; IGG DEFICIENCY; INFANT; INFANT, NEWBORN; INFECTION; MALE; POLYSACCHARIDES, BACTERIAL; SYNDROME;

EID: 0033035244     PISSN: 07368046     EISSN: None     Source Type: Journal    
DOI: 10.1046/j.1525-1470.1999.99005.x     Document Type: Article

References (8)

1. Smith DL, Smith JG, Wong SW, deShazo RD. Netherton's syndrome: a syndrome of elevated IgE and characteristic skin and hair findings. J Allergy Clin Immunol 1995;95: 116-123.
2. Cornel M. Ichthyosis linearis circumflexa. Dermatologica 1949;98:133-136.
3. Netherton EW. A unique case of trichorrhexis nodosa -bamboo hairs. Arch Dermatol 1958;78:483-487.
4. Wilkinson RD, Curtis GH, Hawk WA. Netherton's disease: trichorrhexis invaginata (bamboo hair), congenital ichthyosiform erythroderma and the atopic diasthesis. A histopathologic study. Arch Dermatol 1964;89:46-52.
5. Greene SL, Muller SA. Netherton's syndrome: report of a case and review of the literature. J Am Acad Dermatol 1985;13:329-337.
6. Judge MR, Morgan G, Harper JI. A clinical and immunologic study of Netherton's syndrome. Br J Dermatol 1994; 131:615-621.
7. Knutsen AP. Chronic sinusitis in children. Pediatr Asthma Allergy Immunol 1997;11:147-169.
8. Knutsen AP. Patients with IgG subclass and/or selective antibody deficiency to polysaccharide antigens: initiation of a controlled clinical trial of intravenous immune globulin. J Allergy Clin Immunol 1989;84:640-647.