Astrocytes: Emerging stars in leukodystrophy pathogenesis

Translational Neuroscience

Volumn 4, Issue 2, 2013, Pages 144-164

  Lanciotti, Angela ^a   Brignone, Maria Stefania ^a   Bertini, Enrico ^b   Petrucci, Tamara C ^a   Aloisi, Francesca ^a   Ambrosini, Elena ^a  

^a ISTITUTO SUPERIORE DI SANITÀ   (Italy)

^b BAMBINO GESÙ CHILDREN S HOSPITAL   (Italy)

Author keywords

Alexander's disease; CNS diseases; Glial cells; Ion homeostasis; Leukodystrophies; Megalencephalic leukoencephalopathy with subcortical cysts (MLC); Myelin; Vanishing white matter disease

Indexed keywords

4 AMINOBUTYRIC ACID; ACETYLCHOLINE; ADENOSINE TRIPHOSPHATASE (POTASSIUM); BRAIN DERIVED NEUROTROPHIC FACTOR; DOPAMINE; EXCITATORY AMINO ACID TRANSPORTER; EXCITATORY AMINO ACID TRANSPORTER 2; GLIAL CELL LINE DERIVED NEUROTROPHIC FACTOR; GLIAL FIBRILLARY ACIDIC PROTEIN; GLUTAMATE TRANSPORTER; GLYCINE; LEUKEMIA INHIBITORY FACTOR; MYELIN; NERVE GROWTH FACTOR; NEUROTRANSMITTER; NEUROTROPHIN 3; NORADRENALIN; SEROTONIN; SODIUM ION; SOMATOMEDIN; THROMBOSPONDIN; TISSUE SCAFFOLD;

ALEXANDER DISEASE; ASTROCYTE; BLOOD BRAIN BARRIER; BLOOD VESSEL; BRAIN CYST; BRAIN DISEASE; CELL ACTIVITY; CELL DIFFERENTIATION; CELL FUNCTION; CELL POPULATION; CELL PROLIFERATION; CELL SURVIVAL; CELL VIABILITY; CENTRAL NERVOUS SYSTEM FUNCTION; DEMYELINATION; DISEASE COURSE; ENERGY METABOLISM; EXTRACELLULAR FLUID; GAP JUNCTION; GENE; GENE MUTATION; GFAP GENE; GLIA CELL; HOMEOSTASIS; HUMAN; IN VITRO STUDY; IN VIVO STUDY; LEUKODYSTROPHY; MYELINATION; NERVE DEGENERATION; NERVOUS SYSTEM DEVELOPMENT; NEUROLOGIC DISEASE; NEUROTRANSMISSION; NONHUMAN; OLIGODENDROGLIA; PATHOGENESIS; PATHOPHYSIOLOGY; PRIORITY JOURNAL; PROTEIN BLOOD LEVEL; PROTEIN EXPRESSION; PROTEIN SECRETION; REGULATORY MECHANISM; REVIEW; SYNAPSE; SYNAPTIC TRANSMISSION; SYNAPTOGENESIS; SYNCYTIUM; WHITE MATTER LESION; ARTICLE; NERVE CELL; NUCLEAR MAGNETIC RESONANCE IMAGING; WHITE MATTER;

EID: 84885072578     PISSN: 20813856     EISSN: 20816936     Source Type: Journal    
DOI: 10.2478/s13380-013-0118-1     Document Type: Review

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