Mitochondrial dysfunction and defective autophagy in the pathogenesis of collagen VI muscular dystrophies

Cold Spring Harbor Perspectives in Biology

Volumn 5, Issue 5, 2013, Pages

  Bernardi, Paolo ^a   Bonaldo, Paolo ^a  

^a UNIVERSITY OF PADOVA   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

MUS;

COL6A1 PROTEIN, MOUSE; COLLAGEN TYPE 6;

ANIMAL; AUTOPHAGY; DISEASE MODEL; GENETICS; HUMAN; INTRACELLULAR MEMBRANE; METABOLISM; MITOCHONDRION; MOUSE; MUSCULAR DYSTROPHY; PATHOLOGY; PERMEABILITY; PHYSIOLOGY;

ANIMALS; AUTOPHAGY; COLLAGEN TYPE VI; DISEASE MODELS, ANIMAL; HUMANS; INTRACELLULAR MEMBRANES; MICE; MITOCHONDRIA; MUSCULAR DYSTROPHIES; PERMEABILITY;

EID: 84877149646     PISSN: None     EISSN: 19430264     Source Type: Journal    
DOI: 10.1101/cshperspect.a011387     Document Type: Article

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