Altered threshold of the mitochondrial permeability transition pore in Ullrich congenital muscular dystrophy

Biochimica et Biophysica Acta - Bioenergetics

Volumn 1777, Issue 7-8, 2008, Pages 893-896

  Angelin, Alessia ^a   Bonaldo, Paolo ^a   Bernardi, Paolo ^a  

^a UNIVERSITY OF PADOVA   (Italy)

Author keywords

Collagen VI; Cyclosporin A; Mitochondria; Muscular dystrophy; Permeability transition

Indexed keywords

ADENOSINE TRIPHOSPHATE; CALCIUM; CALCIUM CHELATING AGENT; COLLAGEN TYPE 6; CYCLOSPORIN A; F1FO SYNTHASE; OLIGOMYCIN; PROTON TRANSPORTING ADENOSINE TRIPHOSPHATE SYNTHASE; ROTENONE; THAPSIGARGIN;

ARTICLE; CALCIUM CELL LEVEL; CALCIUM DEPLETION; CELL MEMBRANE DEPOLARIZATION; CELL MEMBRANE PERMEABILITY; CONTROLLED STUDY; DEPLETION; DISEASE SEVERITY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ELECTRON TRANSPORT; GENE MUTATION; HUMAN; HUMAN CELL; MITOCHONDRIAL MEMBRANE; MITOCHONDRIAL MEMBRANE POTENTIAL; MUSCULAR DYSTROPHY; MYOBLAST; POROSITY; PRIORITY JOURNAL; ULLRICH CONGENITAL MUSCULAR DYSTROPHY;

ADENOSINE TRIPHOSPHATE; ANIMALS; CHELATING AGENTS; COLLAGEN; DISEASE MODELS, ANIMAL; EGTAZIC ACID; HUMANS; MEMBRANE POTENTIALS; MICE; MITOCHONDRIA, MUSCLE; MITOCHONDRIAL MEMBRANES; MUSCULAR DYSTROPHIES, LIMB-GIRDLE; MYOBLASTS; OLIGOMYCINS; PERMEABILITY; REFERENCE VALUES; ROTENONE;

EID: 46349109604     PISSN: 00052728     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.bbabio.2008.03.026     Document Type: Article

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