Cyclosporine a in Ullrich congenital muscular dystrophy: Long-term results

Oxidative Medicine and Cellular Longevity

Volumn , Issue , 2011, Pages

  Merlini, Luciano ^a,b   Sabatelli, Patrizia ^c   Armaroli, Annarita ^a   Gnudi, Saverio ^b   Angelin, Alessia ^d   Grumati, Paolo ^d   Michelini, Maria Elena ^e   Franchella, Andrea ^e   Gualandi, Francesca ^a   Bertini, Enrico ^f   Maraldi, Nadir Mario ^b   Ferlini, Alessandra ^a   Bonaldo, Paolo ^d   Bernardi, Paolo ^d  

^a UNIVERSITY OF FERRARA   (Italy)

^b RIZZOLI ORTHOPAEDIC INSTITUTE   (Italy)

^c CNR   (Italy)

^d UNIVERSITY OF PADOVA   (Italy)

^e S ANNA HOSPITAL   (Italy)

^f BAMBINO GESÙ CHILDREN S HOSPITAL   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

APOPTOTIC; CYCLOSPORINE A; MITOCHONDRIAL DYSFUNCTION; MOTOR FUNCTION; MUSCLE REGENERATION; MUSCLE STRENGTH; MUSCULAR DYSTROPHY; RESPIRATORY FUNCTION; RESPIRATORY MUSCLES;

GENES; MUSCLE;

PATIENT TREATMENT;

COLLAGEN TYPE 6; CYCLOSPORIN A; MYOSIN HEAVY CHAIN; CYCLOSPORIN; ENZYME INHIBITOR;

APOPTOSIS; ARTICLE; BODY MASS; BONE DENSITY; BREATHING MUSCLE; CHILD; CLINICAL ARTICLE; CLINICAL TRIAL; DUAL ENERGY X RAY ABSORPTIOMETRY; FORCED VITAL CAPACITY; GENE EXPRESSION; GENE MUTATION; HIRSUTISM; HUMAN; HUMAN TISSUE; IMMUNOHISTOCHEMISTRY; MOTOR PERFORMANCE; MUSCLE BIOPSY; MUSCLE REGENERATION; MUSCLE STRENGTH; MUSCULAR DYSTROPHY; PHENOTYPE; PRESCHOOL CHILD; RESPIRATORY FUNCTION; SCHOOL CHILD; SKIN BIOPSY; ULLRICH CONGENITAL MUSCULAR DYSTROPHY; DRUG EFFECT; FEMALE; GENETICS; MALE; METABOLISM; MITOCHONDRIAL MEMBRANE POTENTIAL; MUTATION; PHYSIOLOGY; REGENERATION; SCLEROSIS; SKELETAL MUSCLE;

APOPTOSIS; CHILD; CHILD, PRESCHOOL; COLLAGEN TYPE VI; CYCLOSPORINE; ENZYME INHIBITORS; FEMALE; HUMANS; MALE; MEMBRANE POTENTIAL, MITOCHONDRIAL; MUSCLE STRENGTH; MUSCLE, SKELETAL; MUSCULAR DYSTROPHIES; MUTATION; REGENERATION; SCLEROSIS;

EID: 84855323182     PISSN: 19420900     EISSN: 19420994     Source Type: Journal    
DOI: 10.1155/2011/139194     Document Type: Article

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