Autophagy is increased in laminin α2 chain-deficient muscle and its inhibition improves muscle morphology in a mouse model of MDC1A

Human Molecular Genetics

Volumn 20, Issue 24, 2011, Pages 4891-4902

  Carmignac, Virginie ^a   Svensson, Martina ^a   Körner, Zandra ^a   Elowsson, Linda ^a   Matsumura, Cintia ^a   Gawlik, Kinga I ^a   Allamand, Valerie ^b,c,d,e   Durbeej, Madeleine ^a  

^a LUND UNIVERSITY   (Sweden)

^b SORBONNE UNIVERSITÉ   (France)

^c CNRS   (France)

^d INSERM   (France)

^e Institut de Myologie   (France)

Author keywords

[No Author keywords available]

Indexed keywords

3 METHYLADENINE; BENZYLOXYCARBONYLLEUCYLLEUCYLLEUCINAL; LAMININ ALPHA2; PROTEASOME; PROTEIN KINASE B;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL TISSUE; APOPTOSIS; ARTICLE; AUTOPHAGY; CONTROLLED STUDY; DRUG EFFECT; FETUS; GENE EXPRESSION; LIFESPAN; LOCOMOTION; LYSOSOME; MORPHOLOGY; MOUSE; MUSCLE ATROPHY; MUSCLE CELL; MUSCLE MASS; MUSCLE REGENERATION; MUSCULAR DYSTROPHY; MYOFIBROSIS; NONHUMAN; PERIPHERAL NEUROPATHY; PHENOTYPE; PRIORITY JOURNAL; PROTEIN DEFICIENCY; PROTEIN DEGRADATION; PROTEIN PHOSPHORYLATION; SURVIVAL RATE; UPREGULATION;

ADENINE; ANIMALS; APOPTOSIS; AUTOPHAGY; BEHAVIOR, ANIMAL; DISEASE MODELS, ANIMAL; DRUG THERAPY, COMBINATION; FIBROSIS; GENE EXPRESSION REGULATION; INJECTIONS; LAMININ; LEUPEPTINS; MICE; MOTOR ACTIVITY; MUSCLES; MUSCULAR ATROPHY; MUSCULAR DYSTROPHIES; PERIPHERAL NERVOUS SYSTEM DISEASES; PHENOTYPE; PHOSPHORYLATION; PROTO-ONCOGENE PROTEINS C-AKT; REGENERATION; SURVIVAL ANALYSIS;

EID: 81855205301     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddr427     Document Type: Article

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