Collagen VI deficiency affects the organization of fibronectin in the extracellular matrix of cultured fibroblasts

Matrix Biology

Volumn 20, Issue 7, 2001, Pages 475-486

  Sabatelli, Patrizia ^a   Bonaldo, Paolo ^b   Lattanzi, Giovanna ^a   Braghetta, Paola ^b   Bergamin, Natascha ^b   Capanni, Cristina ^c   Mattioli, Elisabetta ^c   Columbaro, Marta ^c   Ognibene, Andrea ^c   Pepe, Guglielmina ^d   Bertini, Enrico ^e   Merlini, Luciano ^c   Maraldi, Nadir M ^a,c   Squarzoni, Stefano ^a  

^a CNR   (Italy)

^b UNIVERSITY OF PADOVA   (Italy)

^c RIZZOLI ORTHOPAEDIC INSTITUTE   (Italy)

^d UNIVERSITY OF ROME TOR VERGATA   (Italy)

^e BAMBINO GESÙ CHILDREN S HOSPITAL   (Italy)

Author keywords

Bethlem myopathy; Collagen VI; Extracellular matrix; Fibronectin; Knockout mice

Indexed keywords

COLLAGEN ANTIBODY; COLLAGEN TYPE 6; FIBRONECTIN;

ANIMAL CELL; ANIMAL MODEL; ARTICLE; ASSAY; COLLAGEN VI DEFICIENCY; CONTROLLED STUDY; EXTRACELLULAR MATRIX; FIBROBLAST; HUMAN; HUMAN CELL; IMMUNOELECTRON MICROSCOPY; MOUSE; MYOPATHY; NONHUMAN; PRIORITY JOURNAL; PROTEIN BINDING; PROTEIN DEFICIENCY; PROTEIN INTERACTION; PROTEIN SECRETION; PROTEIN SYNTHESIS;

ANIMALS; BONE MARROW CELLS; CELLS, CULTURED; COLLAGEN TYPE VI; EXTRACELLULAR MATRIX; FIBROBLASTS; FIBRONECTINS; HUMANS; MICE; MICE, KNOCKOUT; MICE, NUDE;

EID: 0034751165     PISSN: 0945053X     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0945-053X(01)00160-3     Document Type: Article

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