Zebrafish models of collagen VI-related myopathies

Human Molecular Genetics

Volumn 19, Issue 12, 2010, Pages 2433-2444

  Telfer, W R ^a   Busta, A S ^a   Bonnemann, C G ^b   Feldman, E L ^a   Dowling, J J ^a  

^a UNIVERSITY OF MICHIGAN HEALTH SYSTEM   (United States)

^b CHILDREN S HOSPITAL OF PHILADELPHIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

COLLAGEN TYPE 6; CYCLOSPORIN A;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL DEATH; COL6A1 GENE; COLLAGEN METABOLISM; CONTROLLED STUDY; ELECTRON MICROSCOPY; EMBRYO; GENE; MUSCLE MITOCHONDRION; MYOPATHY; NONHUMAN; PATHOPHYSIOLOGY; PHENOTYPE; PRIORITY JOURNAL; ZEBRA FISH;

ANIMALS; APOPTOSIS; COLLAGEN TYPE VI; CYCLOSPORINE; DISEASE MODELS, ANIMAL; EMBRYO, NONMAMMALIAN; EXONS; GENE KNOCKDOWN TECHNIQUES; HUMANS; MICE; MITOCHONDRIA, MUSCLE; MOTOR ACTIVITY; MUSCLE, SKELETAL; MUSCULAR DYSTROPHIES; SARCOLEMMA; ZEBRAFISH;

ANIMALIA; DANIO RERIO; MUS; VERTEBRATA;

EID: 77955290564     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddq126     Document Type: Article

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