Collagen VI deficiency induces early onset myopathy in the mouse: An animal model for Bethlem myopathy

Human Molecular Genetics

Volumn 7, Issue 13, 1998, Pages 2135-2140

  Bonaldo, Paolo ^a   Braghetta, Paola ^a   Zanetti, Miriam ^a   Piccolo, Stefano ^a   Volpin, Dino ^a   Bressan, Giorgio M ^a  

^a UNIVERSITY OF PADOVA   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

COLLAGEN TYPE 6;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; COLLAGEN DEFECT; CONTROLLED STUDY; DIAPHRAGM; EMBRYO; FEMALE; GENE DISRUPTION; HETEROZYGOTE; HOMOZYGOTE; MALE; MOUSE; MUSCLE NECROSIS; MUSCLE REGENERATION; MYOPATHY; NEWBORN; NONHUMAN; PHAGOCYTOSIS; PRIORITY JOURNAL;

EID: 0031760509     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/7.13.2135     Document Type: Article

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