Reduction of polyglutamine toxicity by TDP-43, FUS and progranulin in Huntington's disease models

Human Molecular Genetics

Volumn 22, Issue 4, 2013, Pages 782-794

  Tauffenberger, Arnaud ^a,b,c   Chitramuthu, Babykumari P ^d   Bateman, Andrew ^d   Bennett, Hugh PJ ^d   Parker, J Alex ^a,b,c  

^a CENTRE HOSPITALIER DE L UNIVERSITÉ DE MONTRÉAL   (Canada)

^b UNIVERSITY OF MONTREAL   (Canada)

^c UNIVERSITÉ DE MONTRÉAL   (Canada)

^d ROYAL VICTORIA HOSPITAL   (Canada)

Author keywords

[No Author keywords available]

Indexed keywords

ATAXIN 3; FUSED IN SARCOMA PROTEIN; POLYGLUTAMINE; PROGRANULIN; SMALL INTERFERING RNA; TAR DNA BINDING PROTEIN;

ALZHEIMER DISEASE; ARTICLE; BACTERIAL GENETICS; CAENORHABDITIS ELEGANS; EXON; GENE DELETION; GENETIC ANALYSIS; HUNTINGTON CHOREA; IN VIVO STUDY; MAMMAL CELL; NEMATODE; NERVE DEGENERATION; NEUROPROTECTION; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL; PROTEIN AGGREGATION;

ANIMALS; ANIMALS, GENETICALLY MODIFIED; AXONS; CAENORHABDITIS ELEGANS; CAENORHABDITIS ELEGANS PROTEINS; CELL LINE; DISEASE MODELS, ANIMAL; DNA-BINDING PROTEINS; GENE KNOCKDOWN TECHNIQUES; HISTONE DEACETYLASES; HUMANS; HUNTINGTON DISEASE; INTERCELLULAR SIGNALING PEPTIDES AND PROTEINS; MALE; MICE; NERVE TISSUE PROTEINS; NUCLEAR PROTEINS; PEPTIDES; RNA, SMALL INTERFERING;

EID: 84873044588     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/dds485     Document Type: Article

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