SHSP in the eye lens: Crystallin mutations, cataract and proteostasis

International Journal of Biochemistry and Cell Biology

Volumn 44, Issue 10, 2012, Pages 1687-1697

  Clark, Alice R ^a   Lubsen, Nicolette H ^b   Slingsby, Christine ^a  

^a UNIVERSITY OF LONDON   (United Kingdom)

^b RADBOUD UNIVERSITY NIJMEGEN   (Netherlands)

Author keywords

Chaperone; Crystallin; Lens transparency; Myopathy; Small heat shock protein

Indexed keywords

ALPHA CRYSTALLIN; BETA CRYSTALLIN; CHAPERONE; GAMMA CRYSTALLIN; SMALL HEAT SHOCK PROTEIN;

ARTICLE; CATARACT; HUMAN; LENS; MISSENSE MUTATION; MOLECULAR DYNAMICS; MYOPATHY; PROTEIN HOMEOSTASIS; PROTEIN STRUCTURE; SKELETAL MUSCLE;

ANIMALS; BINDING SITES; CATARACT; CRYSTALLINS; HEAT-SHOCK PROTEINS, SMALL; HUMANS; LENS, CRYSTALLINE; MUTATION; PROTEIN CONFORMATION; PROTEOSTASIS DEFICIENCIES; STRESS, PHYSIOLOGICAL;

EID: 84864454491     PISSN: 13572725     EISSN: 18785875     Source Type: Journal    
DOI: 10.1016/j.biocel.2012.02.015     Document Type: Article

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