The cardiomyopathy and lens cataract mutation in αB-crystallin alters its protein structure, chaperone activity, and interaction with intermediate filaments in vitro

Journal of Biological Chemistry

Volumn 274, Issue 47, 1999, Pages 33235-33243

  Der Perng, Ming ^a   Muchowski, Paul J ^b   Van Den IJssel, Paul ^a   Wu, Gabrielle J S ^b   Hutchesont, Aileen M ^a   Clark, John I ^b,c   Quinlan, Roy A ^a  

^a UNIVERSITY OF DUNDEE   (United Kingdom)

^b UNIVERSITY OF WASHINGTON   (United States)

^c UNIVERSITY OF WASHINGTON SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ALPHA CRYSTALLIN; BETA CRYSTALLIN; CHAPERONE; DESMIN; HEAT SHOCK PROTEIN;

ARTICLE; CARDIOMYOPATHY; CATARACT; CIRCULAR DICHROISM; COMPLEX FORMATION; ENZYME SUBSTRATE; GENE MUTATION; INTERMEDIATE FILAMENT; NONHUMAN; PRIORITY JOURNAL; PROTEIN ASSEMBLY; PROTEIN DENATURATION; PROTEIN PROTEIN INTERACTION; PROTEIN STRUCTURE; RECEPTOR BINDING; TARGET CELL;

CARDIOMYOPATHIES; CATARACT; CHYMOTRYPSIN; CIRCULAR DICHROISM; CRYSTALLINS; HUMANS; MICROSCOPY, ELECTRON; MUTAGENESIS; PROTEIN CONFORMATION; RECOMBINANT PROTEINS; SPECTROPHOTOMETRY, ULTRAVIOLET;

EID: 0000843475     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.274.47.33235     Document Type: Article

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