SCOPUS 정보 검색 플랫폼

Volumn 8, Issue 4, 2012, Pages 1197-1205

Impaired dynamics of the late endosome/lysosome compartment in human Niemann-Pick type C skin fibroblasts carrying mutation in NPC1 gene

(5) Sztolsztener, Malgorzata E a Dobrzyn, Agnieszka a Pikula, Slawomir a Tylki Szymanska, Anna b Bandorowicz Pikula, Joanna a

a NENCKI INSTITUTE OF EXPERIMENTAL BIOLOGY (Poland)

b CHILDREN'S MEMORIAL HEALTH INSTITUTE (Poland)

Author keywords

[No Author keywords available]

Indexed keywords

CALPHOBINDIN II; CARRIER PROTEIN; CHOLESTEROL; FATTY ACID; LYSOBISPHOSPHATIDIC ACID; LYSOPHOSPHOLIPID; MEMBRANE PROTEIN; MONOACYLGLYCEROL; NPC1 PROTEIN, HUMAN; SPHINGOMYELIN;

ADULT; ARTICLE; CELL FRACTIONATION; CELL LINE; CELL MEMBRANE; CYTOLOGY; ENDOPLASMIC RETICULUM; ENDOSOME; FEMALE; FIBROBLAST; GENETICS; GOLGI COMPLEX; HUMAN; LIPID METABOLISM; LYSOSOME; MEMBRANE FLUIDITY; METABOLISM; METHODOLOGY; MUTATION; NIEMANN PICK DISEASE; PRESCHOOL CHILD; SKIN; THIN LAYER CHROMATOGRAPHY; TRANSPORT AT THE CELLULAR LEVEL;

ADULT; ANNEXIN A6; BIOLOGICAL TRANSPORT; CARRIER PROTEINS; CELL FRACTIONATION; CELL LINE; CELL MEMBRANE; CHILD, PRESCHOOL; CHOLESTEROL; CHROMATOGRAPHY, THIN LAYER; ENDOPLASMIC RETICULUM; ENDOSOMES; FATTY ACIDS; FEMALE; FIBROBLASTS; GOLGI APPARATUS; HUMANS; LIPID METABOLISM; LYSOPHOSPHOLIPIDS; LYSOSOMES; MEMBRANE FLUIDITY; MEMBRANE GLYCOPROTEINS; MONOGLYCERIDES; MUTATION; NIEMANN-PICK DISEASE, TYPE C; SKIN; SPHINGOMYELINS;

EID: 84858012282 PISSN: 1742206X EISSN: 17422051 Source Type: Journal
DOI: 10.1039/c2mb05447g Document Type: Article

Times cited : (16)

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