Biochemistry of glycosphingolipid degradation

Clinica Chimica Acta

Volumn 266, Issue 1, 1997, Pages 51-61

  Sandhoff, Konrad ^a   Kolter, Thomas ^a  

^a UNIVERSITY OF BONN   (Germany)

Author keywords

Glycosphingolipids; Lysosomes; Sphingolipid activator proteins; Sphingolipidoses; Storage diseases

Indexed keywords

GANGLIOSIDE GM2; GLYCOSPHINGOLIPID; HYDROLASE; SPHINGOLIPID ACTIVATOR PROTEIN;

CELL SURFACE; CONFERENCE PAPER; ENDOCYTOSIS; EUKARYOTIC CELL; HUMAN; LIPIDOSIS; LYSOSOME; LYSOSOME MEMBRANE; MEMBRANE DAMAGE; MEMBRANE STRUCTURE; NONHUMAN; PRIORITY JOURNAL; STORAGE DISEASE;

ANIMALS; DISEASE MODELS, ANIMAL; ENDOCYTOSIS; G(M2) ACTIVATOR PROTEIN; G(M2) GANGLIOSIDE; GLYCOSPHINGOLIPIDS; HUMANS; HYDROLYSIS; LYSOSOMES; PROTEINS; TAY-SACHS DISEASE;

EUKARYOTA;

EID: 0030727680     PISSN: 00098981     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0009-8981(97)00166-6     Document Type: Conference Paper

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