Lipid and cholesterol trafficking in NPC

Biochimica et Biophysica Acta - Molecular and Cell Biology of Lipids

Volumn 1685, Issue 1-3, 2004, Pages 28-37

  Mukherjee, Sushmita ^a   Maxfield, Frederick R ^a  

^a WEILL CORNELL MEDICAL COLLEGE   (United States)

Author keywords

Endocytosis; Membrane domain; Niemann Pick C; NPC1; Sphingolipid storage disorder

Indexed keywords

25 HYDROXYCHOLESTEROL; 3BETA (2 DIETHYLAMINOETHOXY)ANDROST 5 EN 17 ONE; 7 OXOCHOLESTEROL; AMPHOPHILE; CHOLESTEROL; LIPID; TOLNAFTATE;

BIOSYNTHESIS; BONE MARROW TRANSPLANTATION; CELL CYCLE; CELL MEMBRANE; CELL ORGANELLE; CHILDHOOD DISEASE; CHOLESTEROL METABOLISM; CHOLESTEROL TRANSPORT; CLINICAL FEATURE; CRYSTAL STRUCTURE; DEGENERATIVE DISEASE; DIET THERAPY; ENDOPLASMIC RETICULUM; ENDOSOME; ENZYME REPLACEMENT; FIBROBLAST; GENE THERAPY; GENETIC ANALYSIS; GOLGI COMPLEX; HUMAN; INTRACELLULAR TRANSPORT; LIPID ANALYSIS; LIPID STORAGE; LIPID TRANSPORT; MAMMAL CELL; MOLECULAR GENETICS; NERVE CELL; NIEMANN PICK DISEASE; NONHUMAN; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN DEGRADATION; PROTEIN DOMAIN; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN TARGETING; REVIEW;

ANIMALS; BIOLOGICAL TRANSPORT; BIOPHYSICS; CARRIER PROTEINS; CHOLESTEROL; ENDOCYTOSIS; ENDOPLASMIC RETICULUM; ENDOSOMES; GLYCOPROTEINS; HUMANS; LIPID METABOLISM; LYSOSOMES; MEMBRANE GLYCOPROTEINS; MODELS, BIOLOGICAL; NIEMANN-PICK DISEASES;

EID: 4744376060     PISSN: 13881981     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.bbalip.2004.08.009     Document Type: Review

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