Primary immunodeficiency associated with defects in CD1 and CD1-restricted T cells

Annals of the New York Academy of Sciences

Volumn 1250, Issue 1, 2012, Pages 14-24

  Zeissig, Sebastian ^a,b   Blumberg, Richard S ^a  

^a BRIGHAM AND WOMEN S HOSPITAL   (United States)

^b UNIVERSITY OF KIEL   (Germany)

Author keywords

CD1; CD1d; Lipid antigen presentation; Natural killer T cells

Indexed keywords

ADAPTOR PROTEIN; APOLIPOPROTEIN B; AUTOIMMUNE REGULATOR PROTEIN; BETA GALACTOSIDASE; CD1 ANTIGEN; CD150 ANTIGEN; INTERLEUKIN 1 RECEPTOR ASSOCIATED KINASE 4; LIPID; LIPID TRANSFER PROTEIN; MICROSOMAL TRIGLYCERIDE TRANSFER PROTEIN; PROSAPOSIN; PROTEIN TYROSINE KINASE; RAG1 PROTEIN; RAG2 PROTEIN; SIGNALING LYMPHOCYTE ACTIVATION MOLECULE ASSOCIATED PROTEIN; VERY LOW DENSITY LIPOPROTEIN; WISKOTT ALDRICH SYNDROME PROTEIN;

ABETALIPOPROTEINEMIA; APOPTOSIS; ARTICLE; AUTOIMMUNE POLYENDOCRINOPATHY CANDIDIASIS ECTODERMAL DYSTROPHY; B LYMPHOCYTE; CD4+ T LYMPHOCYTE; CD8+ T LYMPHOCYTE; CELL ACTIVATION; CELL DAMAGE; CELL MATURATION; CELLULAR IMMUNITY; COMMON VARIABLE IMMUNODEFICIENCY; CYTOKINE PRODUCTION; CYTOMEGALOVIRUS; DENDRITIC CELL; DISEASE PREDISPOSITION; ENDOPLASMIC RETICULUM; ENTERITIS; EPSTEIN BARR VIRUS INFECTION; GAUCHER DISEASE; GENE DELETION; GENETIC CODE; GM1 GANGLIOSIDOSIS; HERPES SIMPLEX VIRUS 1; HERPES SIMPLEX VIRUS 2; HERPES ZOSTER; HYPOBETALIPOPROTEINEMIA; IMMUNE DEFICIENCY; INSULIN DEPENDENT DIABETES MELLITUS; LIPID DEGRADATION; LIPID TRANSPORT; LYMPHOCYTE COUNT; LYMPHOCYTE FUNCTION; LYMPHOCYTE PROLIFERATION; LYMPHOCYTE SUBPOPULATION; LYMPHOPROLIFERATIVE DISEASE; LYSOSOME; MACROPHAGE; METACHROMATIC LEUKODYSTROPHY; NATURAL KILLER T CELL; NIEMANN PICK DISEASE; NONHUMAN; OCULAR ALBINISM; OMENN SYNDROME; PHENOTYPE; PROTEIN EXPRESSION; SIGNAL TRANSDUCTION; TAY SACHS DISEASE; VARICELLA ZOSTER VIRUS; WISKOTT ALDRICH SYNDROME;

MUS;

EID: 84857499431     PISSN: 00778923     EISSN: 17496632     Source Type: Book Series    
DOI: 10.1111/j.1749-6632.2011.06380.x     Document Type: Article

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