Fatal Epstein-Barr virus infection in a case of familial hemophagocytic lymphohistiocytosis with syntaxin-11 mutation

Turkish Journal of Pediatrics

Volumn 51, Issue 4, 2009, Pages 371-374

  Albayrak, Meryem ^a   Kaya, Zühre ^a   Yilmaz Keskin, Ebru ^a   Stadt, Udo Zur ^b   Koçak, Ülker ^a   Gürsel, Türkiz ^a  

^a GAZI UNIVERSITY FACULTY OF MEDICINE   (Turkey)

^b UNIVERSITY MEDICAL CENTER HAMBURG EPPENDORF   (Germany)

Author keywords

Child; Epstein Barr virus; Familial hemophagocytic lymphohistiocytosis; Syntaxin 11 mutation

Indexed keywords

ACICLOVIR; ALANINE AMINOTRANSFERASE; ANTIBIOTIC AGENT; ASPARTATE AMINOTRANSFERASE; CYCLOSPORIN A; IMMUNOGLOBULIN; MEMBRANE PROTEIN; PERFORIN; PROTEIN MUNC13 4; SYNTAXIN; SYNTAXIN 11; TRIACYLGLYCEROL; UNCLASSIFIED DRUG;

ABDOMINAL DISTENSION; ARTICLE; BLOOD CLOTTING DISORDER; CASE REPORT; CHILD; EPSTEIN BARR VIRUS; FEVER; GENE MUTATION; HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS; HEPATOMEGALY; HUMAN; HYPERFERRITINEMIA; HYPERLIPIDEMIA; HYPOFIBRINOGENEMIA; MALE; NATURAL KILLER CELL; NEUTROPHIL COUNT; PANCYTOPENIA; PRESCHOOL CHILD; PROGNOSIS; SPLENOMEGALY; STOP CODON; THROMBOCYTE COUNT; VIRUS INFECTION;

CHILD; CONSANGUINITY; EPSTEIN-BARR VIRUS INFECTIONS; FATAL OUTCOME; HUMANS; LYMPHOHISTIOCYTOSIS, HEMOPHAGOCYTIC; MALE; PROGNOSIS; QA-SNARE PROTEINS;

EID: 70649090277     PISSN: 00414301     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

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