Disruption of axonal transport in motor neuron diseases

International Journal of Molecular Sciences

Volumn 13, Issue 1, 2012, Pages 1225-1238

  Ikenaka, Kensuke ^a   Katsuno, Masahisa ^a   Kawai, Kaori ^a   Ishigaki, Shinsuke ^a,b   Tanaka, Fumiaki ^a   Sobue, Gen ^a,b  

^a NAGOYA UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

^b JAPAN SCIENCE AND TECHNOLOGY AGENCY   (Japan)

Author keywords

Amyotrophic lateral sclerosis; Axonal transport; Dynactin 1; Dynein; Hereditary spastic paraplegia; Kinesin; Motor neuron; Neurofilament; Spinal and bulbar muscular atrophy; Spinal muscular atrophy

Indexed keywords

ALSIN PROTEIN; ANDROGEN RECEPTOR; ATLASTIN PROTEIN; AXONEMAL DYNEIN; BRAIN PROTEIN; CHARGED MULTIVESICULAR BODY PROTEIN 2B; COPPER ZINC SUPEROXIDE DISMUTASE; DYNACTIN 1 PROTEIN; KINESIN; MESSENGER RNA; MULTIPROTEIN COMPLEX; MUTANT PROTEIN; SPASTIN; STRESS ACTIVATED PROTEIN KINASE; SYNAPTOBREVIN ASSOCIATED MEMBRANE PROTEIN B; UNCLASSIFIED DRUG; DYNACTIN; DYNEIN ADENOSINE TRIPHOSPHATASE; MICROTUBULE ASSOCIATED PROTEIN;

ALS2 GENE; AMYOTROPHIC LATERAL SCLEROSIS; AR GENE; ARTICLE; ATL1 GENE; AUTOPHAGOSOME; AUTOPSY; CHMP2B GENE; CLINICAL FEATURE; DCTN1 GENE; DEGENERATIVE DISEASE; DISEASE MODEL; DOWN REGULATION; ENZYME ACTIVATION; GENE; GENE EXPRESSION PROFILING; GENE MUTATION; GENETIC CODE; HEREDITARY MOTOR SENSORY NEUROPATHY; HUMAN; KENNEDY DISEASE; KIF5A GENE; MICROTUBULE; MITOCHONDRION; MOTOR NEURON DISEASE; MOTOR SYSTEM; MUTANT; NERVE CELL DEGENERATION; NERVE FIBER TRANSPORT; NEUROFILAMENT; NEUROLOGIC DISEASE; NONHUMAN; NUCLEOTIDE REPEAT; PATHOGENESIS; PHENOTYPE; PROTEIN BINDING; PROTEIN DEPLETION; PROTEIN FUNCTION; SOD1 GENE; SPAST GENE; SPINAL CORD NERVE CELL; SPINAL MUSCULAR ATROPHY; VAPB GENE; ANIMAL; CHEMISTRY; INTERMEDIATE FILAMENT; METABOLISM; NERVE FIBER; PATHOLOGY; PHYSIOLOGY;

RODENTIA;

ANIMALS; AXONAL TRANSPORT; AXONS; DYNEINS; HUMANS; INTERMEDIATE FILAMENTS; KINESIN; MICROTUBULE-ASSOCIATED PROTEINS; MITOCHONDRIA; MOTOR NEURON DISEASE;

EID: 84856281690     PISSN: None     EISSN: 14220067     Source Type: Journal    
DOI: 10.3390/ijms13011225     Document Type: Article

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