Genotype-, aging-dependent abnormal caspase activity in Huntington disease blood cells

Journal of Neural Transmission

Volumn 118, Issue 11, 2011, Pages 1599-1607

  Squitieri, Ferdinando ^a   Maglione, Vittorio ^b   Orobello, Sara ^a   Fornai, Francesco ^a,c  

^a IRCCS NEUROMED   (Italy)

^b UNIVERSITY OF ALBERTA   (Canada)

^c UNIVERSITY OF PISA   (Italy)

Author keywords

Abnormal mitochondria; Caspase activities; Homozygous CAG mutations; Huntingtin (htt) dosage effect; Juvenile Huntington disease (JHD)

Indexed keywords

CASPASE 2; CASPASE 3; CASPASE 6; CASPASE 8; CASPASE 9;

ADULT; AGED; ARTICLE; BLOOD CELL; CELL VIABILITY; CLINICAL ARTICLE; CONTROLLED STUDY; DISEASE COURSE; ENZYME ACTIVITY; FEMALE; GENE MUTATION; GENOTYPE; HETEROZYGOSITY; HOMOZYGOSITY; HUMAN; HUMAN CELL; HUMAN TISSUE; HUNTINGTON CHOREA; MALE; MITOCHONDRION; MORPHOLOGY; PRIORITY JOURNAL;

AGED; AGING; ANIMALS; CASPASES; CHILD; ENZYME ACTIVATION; FEMALE; GENOTYPE; HUMANS; HUNTINGTON DISEASE; LEUKOCYTES; MALE; MICE; MIDDLE AGED; NERVE TISSUE PROTEINS; PRIMARY CELL CULTURE; YOUNG ADULT;

EID: 84855226995     PISSN: 03009564     EISSN: 14351463     Source Type: Journal    
DOI: 10.1007/s00702-011-0646-1     Document Type: Article

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