Comparison of huntingtin proteolytic fragments in human lymphoblast cell lines and human brain

Journal of Neurochemistry

Volumn 82, Issue 1, 2002, Pages 84-92

  Toneff, Thomas ^a   Mende Mueller, Liane ^b   Wu, Ying ^d   Hwang, Shin Rong ^a   Bundey, Richard ^a   Thompson, Leslie M ^c   Chesselet, Marie Francoise ^d   Hook, Vivian ^a,b  

^a BUCK INSTITUTE FOR RESEARCH ON AGING   (United States)

^b UNIVERSITY OF CALIFORNIA   (United States)

^c UNIVERSITY OF CALIFORNIA   (United States)

^d UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

Brain; Huntingtin; Huntington's disease; Lymphoblasts; Proteolysis; Triplet nucleotide repeat

Indexed keywords

AMINO TERMINAL SEQUENCE; ARTICLE; BRAIN; BRAIN CORTEX; CARBOXY TERMINAL SEQUENCE; CONTROLLED STUDY; CORPUS STRIATUM; GENE MUTATION; GENETIC TRANSFECTION; HETEROZYGOSITY; HOMOZYGOSITY; HUMAN; HUMAN CELL; HUNTINGTON CHOREA; LYMPHOBLAST; MOUSE; NEUROTOXICITY; NONHUMAN; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN DOMAIN; TRANSGENIC MOUSE;

AGE OF ONSET; AGED; BLOTTING, WESTERN; BRAIN; BRAIN CHEMISTRY; CELL LINE; HUMANS; HUNTINGTON DISEASE; LYMPHOCYTES; MIDDLE AGED; NERVE TISSUE PROTEINS; NUCLEAR PROTEINS; PEPTIDE FRAGMENTS; PEPTIDE HYDROLASES; POLYMERASE CHAIN REACTION; TRINUCLEOTIDE REPEAT EXPANSION;

MUS MUSCULUS;

EID: 0036314167     PISSN: 00223042     EISSN: None     Source Type: Journal    
DOI: 10.1046/j.1471-4159.2002.00940.x     Document Type: Article

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