GSH monoethyl ester rescues mitochondrial defects in cystic fibrosis models

Human Molecular Genetics

Volumn 20, Issue 14, 2011, Pages 2745-2759

  Kelly Aubert, Mairead ^a   Trudel, Stéphanie ^a   Fritsch, Janine ^a   Nguyen Khoa, Thao ^a,b   Baudouin Legros, Maryvonne ^a   Moriceau, Sandra ^a   Jeanson, Ludovic ^a   Djouadi, Fatima ^a   Matar, Corine ^c   Conti, Marc ^c   Ollero, Mario ^a   Brouillard, Franck ^a   Edelman, Aleksander ^a  

^a UNIVERSITÉ PARIS DESCARTES   (France)

^b HÔPITAL NECKER ENFANTS MALADES   (France)

^c UNIVERSITÉ PARIS EST CRÉTEIL   (France)

Author keywords

[No Author keywords available]

Indexed keywords

5 CHLOROMETHYL 2',7' DICHLORODIHYDROFLUORESCEIN DIACETATEACETYLESTER; ACONITATE HYDRATASE; DICARBOXYLIC ACID; FLUORESCENT DYE; GLUTATHIONE; GLUTATHIONE ETHYL ESTER; INTERLEUKIN 8; IRON; OXOGLUTARATE DEHYDROGENASE; REACTIVE OXYGEN METABOLITE; REDOX EFFECTOR FACTOR 1; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE; TRANSMEMBRANE CONDUCTANCE REGULATOR; UBIQUINONE DERIVATIVE; UNCLASSIFIED DRUG; VITRONECTIN;

ARTICLE; COLON MUCOSA; CONTROLLED STUDY; CYSTIC FIBROSIS; CYTOKINE RELEASE; DEPOLARIZATION; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENZYME ACTIVITY; GENE MUTATION; HETEROZYGOTE; HOMEOSTASIS; HUMAN; HUMAN CELL; INFLAMMATION; MALE; MITOCHONDRIAL MEMBRANE POTENTIAL; MITOCHONDRIAL REDUCED GLUTATHIONE DEPLETION; MITOCHONDRION; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROTEIN TRANSPORT; RESPIRATORY CHAIN;

ANIMALS; CELL LINE; CYSTIC FIBROSIS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; DICARBOXYLIC ACID TRANSPORTERS; ELECTRON TRANSPORT COMPLEX I; GLUTATHIONE; INTERLEUKIN-8; MALE; MEMBRANE POTENTIAL, MITOCHONDRIAL; MEMBRANE TRANSPORT PROTEINS; MICE; MICE, INBRED CFTR; MICE, KNOCKOUT; MITOCHONDRIA; MUTATION; RADIATION-PROTECTIVE AGENTS; RECOVERY OF FUNCTION;

MUS;

EID: 79959829336     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddr173     Document Type: Article

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