Automated spectrophotometric analysis of mitochondrial respiratory chain complex enzyme activities in cultured skin fibroblasts

Clinical Chemistry

Volumn 51, Issue 11, 2005, Pages 2110-2116

  Kramer, Karen A ^a   Oglesbee, Devin ^a   Hartman, Stacy J ^a   Huey, Joe ^a   Anderson, Bambi ^a   Magera, Mark J ^a   Matern, Dietrich ^a   Rinaldo, Piero ^a   Robinson, Brian H ^b   Cameron, Jessie M ^b   Hahn, Si Houn ^a,c  

^a Mayo Clinic   (United States)

^b HOSPITAL FOR SICK CHILDREN RESEARCH INSTITUTE   (Canada)

^c MAYO CLINIC   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CYTOCHROME C OXIDASE; MONOCLONAL ANTIBODY; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE (UBIQUINONE); SUCCINATE DEHYDROGENASE (UBIQUINONE); UBIQUINOL CYTOCHROME C REDUCTASE;

ANALYTIC METHOD; ARTICLE; CELL CULTURE; CLINICAL ARTICLE; CLINICAL PRACTICE; COMPLEX I DEFICIENCY; COMPLEX II DEFICIENCY; COMPLEX III DEFICIENCY; CONTROLLED STUDY; CYTOCHROME C OXIDASE DEFICIENCY; DIAGNOSTIC ACCURACY; DIAGNOSTIC PROCEDURE; DIAGNOSTIC VALUE; ENZYME ACTIVITY; ENZYME SUBUNIT; EVALUATION; HUMAN; HUMAN CELL; IMMUNOBLOTTING; IN VITRO STUDY; LABORATORY AUTOMATION; MITOCHONDRIAL RESPIRATION; MUSCLE BIOPSY; PHENOTYPE; RESPIRATORY CHAIN; SKIN FIBROBLAST; SPECTROPHOTOMETER; SPECTROPHOTOMETRY;

AUTOANALYSIS; BLOTTING, WESTERN; CELLS, CULTURED; ELECTRON TRANSPORT COMPLEX I; ELECTRON TRANSPORT COMPLEX II; ELECTRON TRANSPORT COMPLEX III; ELECTRON TRANSPORT COMPLEX IV; FIBROBLASTS; HUMANS; REFERENCE VALUES; SKIN; SPECTROPHOTOMETRY;

EID: 27444446745     PISSN: 00099147     EISSN: None     Source Type: Journal    
DOI: 10.1373/clinchem.2005.050146     Document Type: Article

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