-
1
-
-
0027480960
-
A novel gene containing a trinucleotide repeat that is expanded and unstable on Huntington's disease chromosomes
-
The Huntington's Research Collaborative Research Group
-
The Huntington's Research Collaborative Research Group A novel gene containing a trinucleotide repeat that is expanded and unstable on Huntington's disease chromosomes. Cell 1993, 72:971-983.
-
(1993)
Cell
, vol.72
, pp. 971-983
-
-
-
3
-
-
67650095269
-
Beyond the brain: widespread pathology in Huntington's disease
-
van der Burg J.M.M., Björkqvist M., Brundin P. Beyond the brain: widespread pathology in Huntington's disease. Lancet Neurol 2009, 8:765-774.
-
(2009)
Lancet Neurol
, vol.8
, pp. 765-774
-
-
van der Burg, J.M.M.1
Björkqvist, M.2
Brundin, P.3
-
4
-
-
0031044805
-
Energy metabolism defects in Huntington's disease and effects of coenzyme Q10
-
Koroshetz W.J., Jenkins B.G., Rosen B.R., Beal M.F. Energy metabolism defects in Huntington's disease and effects of coenzyme Q10. Ann Neurol 1997, 41:160-165.
-
(1997)
Ann Neurol
, vol.41
, pp. 160-165
-
-
Koroshetz, W.J.1
Jenkins, B.G.2
Rosen, B.R.3
Beal, M.F.4
-
5
-
-
0033914747
-
Abnormal in vivo skeletal muscle energy metabolism in Huntington's disease and dentatorubropallidoluysian atrophy
-
Lodi R., Schapira A.H.V., Manners D., Styles P., Wood N.W., Taylor D.J., et al. Abnormal in vivo skeletal muscle energy metabolism in Huntington's disease and dentatorubropallidoluysian atrophy. Ann Neurol 2000, 48:72-76.
-
(2000)
Ann Neurol
, vol.48
, pp. 72-76
-
-
Lodi, R.1
Schapira, A.H.V.2
Manners, D.3
Styles, P.4
Wood, N.W.5
Taylor, D.J.6
-
6
-
-
0029875381
-
Mitochondrial defect in Huntington's disease caudate nucleus
-
Gu M., Gash M.T., Mann V.M., Javoy-Agid F., Cooper J.M., Schapira A.H. Mitochondrial defect in Huntington's disease caudate nucleus. Ann Neurol 1996, 39:385-389.
-
(1996)
Ann Neurol
, vol.39
, pp. 385-389
-
-
Gu, M.1
Gash, M.T.2
Mann, V.M.3
Javoy-Agid, F.4
Cooper, J.M.5
Schapira, A.H.6
-
7
-
-
0030919567
-
Oxidative damage and metabolic dysfunction in Huntington's disease: selective vulnerability of the basal ganglia
-
Browne S.E., Bowling A.C., MacGarvey U., Baik M.J., Berger S.C., Muqit M.M.K., et al. Oxidative damage and metabolic dysfunction in Huntington's disease: selective vulnerability of the basal ganglia. Ann Neurol 1997, 41:646-653.
-
(1997)
Ann Neurol
, vol.41
, pp. 646-653
-
-
Browne, S.E.1
Bowling, A.C.2
MacGarvey, U.3
Baik, M.J.4
Berger, S.C.5
Muqit, M.M.K.6
-
8
-
-
0032851595
-
Increased apoptosis of Huntington disease lymphoblasts associated with repeat length-dependent mitochondrial depolarization
-
Sawa A., Wiegand G.W., Cooper J., Margolis R.L., Sharp A.H., Lawler J.F., et al. Increased apoptosis of Huntington disease lymphoblasts associated with repeat length-dependent mitochondrial depolarization. Nat Med 1999, 5:1194-1198.
-
(1999)
Nat Med
, vol.5
, pp. 1194-1198
-
-
Sawa, A.1
Wiegand, G.W.2
Cooper, J.3
Margolis, R.L.4
Sharp, A.H.5
Lawler, J.F.6
-
9
-
-
70349705584
-
Adenosine, ketogenic diet and epilepsy: the emerging therapeutic relationship between metabolism and brain activity
-
Masino S.A., Kawamura M., Wasser C.D., Pomeroy L.T., Ruskin D.N. Adenosine, ketogenic diet and epilepsy: the emerging therapeutic relationship between metabolism and brain activity. Curr Neuropharmacol 2009, 7:257-268.
-
(2009)
Curr Neuropharmacol
, vol.7
, pp. 257-268
-
-
Masino, S.A.1
Kawamura, M.2
Wasser, C.D.3
Pomeroy, L.T.4
Ruskin, D.N.5
-
10
-
-
1042299789
-
The therapeutic implications of ketone bodies: the effects of ketone bodies in pathological conditions: ketosis, ketogenic diet, redox states, insulin resistance, and mitochondrial metabolism
-
Veech R.L. The therapeutic implications of ketone bodies: the effects of ketone bodies in pathological conditions: ketosis, ketogenic diet, redox states, insulin resistance, and mitochondrial metabolism. Prostaglandins Leukot Essent Fatty Acids 2004, 70:309-319.
-
(2004)
Prostaglandins Leukot Essent Fatty Acids
, vol.70
, pp. 309-319
-
-
Veech, R.L.1
-
11
-
-
27644461807
-
Age-dependent reduction of cortical contusion volume by ketones after traumatic brain injury
-
Prins M.L., Fujima L.S., Hovda D.A. Age-dependent reduction of cortical contusion volume by ketones after traumatic brain injury. J Neurosci Res 2005, 82:413-420.
-
(2005)
J Neurosci Res
, vol.82
, pp. 413-420
-
-
Prins, M.L.1
Fujima, L.S.2
Hovda, D.A.3
-
12
-
-
60249102843
-
Ketogenic diet reduces cytochrome c release and cellular apoptosis following traumatic brain injury in juvenile rats
-
Hu Z.G., Wang H.D., Jin W., Yin H.X. Ketogenic diet reduces cytochrome c release and cellular apoptosis following traumatic brain injury in juvenile rats. Ann Clin Lab Sci 2009, 39:76-83.
-
(2009)
Ann Clin Lab Sci
, vol.39
, pp. 76-83
-
-
Hu, Z.G.1
Wang, H.D.2
Jin, W.3
Yin, H.X.4
-
13
-
-
46649116715
-
Ketogenic diet prevents cardiac arrest-induced cerebral ischemic neurodegeneration
-
Tai K.-K., Nguyen N., Pham L., Truong D.D. Ketogenic diet prevents cardiac arrest-induced cerebral ischemic neurodegeneration. J Neural Transm 2008, 115:1011-1017.
-
(2008)
J Neural Transm
, vol.115
, pp. 1011-1017
-
-
Tai, K.-K.1
Nguyen, N.2
Pham, L.3
Truong, D.D.4
-
14
-
-
56649091297
-
Neuroprotection in diet-induced ketotic rat brain after focal ischemia
-
Puchowicz M.A., Zechel J.L., Valerio J., Emancipator D.S., Xu K., Pundik S., et al. Neuroprotection in diet-induced ketotic rat brain after focal ischemia. J Cereb Blood Flow Metab 2008, 28:1907-1916.
-
(2008)
J Cereb Blood Flow Metab
, vol.28
, pp. 1907-1916
-
-
Puchowicz, M.A.1
Zechel, J.L.2
Valerio, J.3
Emancipator, D.S.4
Xu, K.5
Pundik, S.6
-
15
-
-
22144477541
-
Ketogenic diet reduces hypoglycemia-induced neuronal death in young rats
-
Yamada K.A., Rensing N., Thio L.L. Ketogenic diet reduces hypoglycemia-induced neuronal death in young rats. Neurosci Lett 2005, 385:210-214.
-
(2005)
Neurosci Lett
, vol.385
, pp. 210-214
-
-
Yamada, K.A.1
Rensing, N.2
Thio, L.L.3
-
16
-
-
33745816384
-
A ketogenic diet as a potential novel therapeutic intervention in amyotrophic lateral sclerosis
-
Zhao Z., Lange D.J., Voustianiouk A., MacGrogan D., Ho L., Suh J., et al. A ketogenic diet as a potential novel therapeutic intervention in amyotrophic lateral sclerosis. BMC Neurosci 2006, 7:29.
-
(2006)
BMC Neurosci
, vol.7
, pp. 29
-
-
Zhao, Z.1
Lange, D.J.2
Voustianiouk, A.3
MacGrogan, D.4
Ho, L.5
Suh, J.6
-
17
-
-
77956972404
-
Neuroprotective and anti-inflammatory activities of ketogenic diet on MPTP-induced neurotoxicity
-
Yang X., Cheng B. Neuroprotective and anti-inflammatory activities of ketogenic diet on MPTP-induced neurotoxicity. J Mol Neurosci 2010, 42:145-153.
-
(2010)
J Mol Neurosci
, vol.42
, pp. 145-153
-
-
Yang, X.1
Cheng, B.2
-
18
-
-
76849106773
-
D-β-hydroxybutyrate prevents MPP+-induced neurotoxicity in PC12 cells
-
Cheng B., Yang X., Chen C., Cheng D., Xu X., Zhang X. d-β-hydroxybutyrate prevents MPP+-induced neurotoxicity in PC12 cells. Neurochem Res 2010, 35:444-451.
-
(2010)
Neurochem Res
, vol.35
, pp. 444-451
-
-
Cheng, B.1
Yang, X.2
Chen, C.3
Cheng, D.4
Xu, X.5
Zhang, X.6
-
19
-
-
33845417298
-
Ketogenic diet protects the hippocampus from kainic acid toxicity by inhibiting the dissociation of Bad from 14-3-3
-
Noh H.S., Kim Y.S., Kim Y.H., Han J.Y., Park C.H., Kang A.K., et al. Ketogenic diet protects the hippocampus from kainic acid toxicity by inhibiting the dissociation of Bad from 14-3-3. J Neurosci Res 2006, 84:1829-1836.
-
(2006)
J Neurosci Res
, vol.84
, pp. 1829-1836
-
-
Noh, H.S.1
Kim, Y.S.2
Kim, Y.H.3
Han, J.Y.4
Park, C.H.5
Kang, A.K.6
-
20
-
-
0032030911
-
β-hydroxybutyrate fuels synaptic function during development - histological and physiological evidence in rat hippocampal slices
-
Izumi Y., Ishii K., Benz A.M., Zorumski C.F. β-hydroxybutyrate fuels synaptic function during development - histological and physiological evidence in rat hippocampal slices. J Clin Invest 1998, 101:1121-1132.
-
(1998)
J Clin Invest
, vol.101
, pp. 1121-1132
-
-
Izumi, Y.1
Ishii, K.2
Benz, A.M.3
Zorumski, C.F.4
-
21
-
-
0034624968
-
D-β-Hydroxybutyrate protects neurons in models of Alzheimer's and Parkinson's disease
-
Kashiwaya Y., Takeshima T., Mori N., Nakashima K., Clarke K., Veech R.L. d-β-Hydroxybutyrate protects neurons in models of Alzheimer's and Parkinson's disease. Proc Natl Acad Sci USA 2000, 97:5440-5444.
-
(2000)
Proc Natl Acad Sci USA
, vol.97
, pp. 5440-5444
-
-
Kashiwaya, Y.1
Takeshima, T.2
Mori, N.3
Nakashima, K.4
Clarke, K.5
Veech, R.L.6
-
22
-
-
33746848935
-
Mitochondrial biogenesis in the anticonvulsant mechanism of the ketogenic diet
-
Bough K.J., Wetherington J., Hassel B., Pare J.F., Gawryluk J.W., Greene J.G., et al. Mitochondrial biogenesis in the anticonvulsant mechanism of the ketogenic diet. Ann Neurol 2006, 60:223-235.
-
(2006)
Ann Neurol
, vol.60
, pp. 223-235
-
-
Bough, K.J.1
Wetherington, J.2
Hassel, B.3
Pare, J.F.4
Gawryluk, J.W.5
Greene, J.G.6
-
23
-
-
77952485613
-
Ketogenic diet slows down mitochondrial myopathy progression in mice
-
Ahola-Erkkilä S., Carroll C., Peltola-Mjösund K., Tulkki V., Mattila I., Seppänen-Laasko T., et al. Ketogenic diet slows down mitochondrial myopathy progression in mice. Hum Mol Genet 2010, 19:1974-1984.
-
(2010)
Hum Mol Genet
, vol.19
, pp. 1974-1984
-
-
Ahola-Erkkilä, S.1
Carroll, C.2
Peltola-Mjösund, K.3
Tulkki, V.4
Mattila, I.5
Seppänen-Laasko, T.6
-
24
-
-
34548168613
-
Low carbohydrate ketogenic diet enhances cardiac tolerance to global ischemia
-
Al-Zaid N.S., Dashti H.M., Mathew T.C., Juggi J.S. Low carbohydrate ketogenic diet enhances cardiac tolerance to global ischemia. Acta Cardiol 2007, 62:381-389.
-
(2007)
Acta Cardiol
, vol.62
, pp. 381-389
-
-
Al-Zaid, N.S.1
Dashti, H.M.2
Mathew, T.C.3
Juggi, J.S.4
-
25
-
-
0017954660
-
Chronic ketosis and cerebral metabolism
-
DeVivo D.C., Leckie M.P., Ferrendelli J.S., McDougal D.B. Chronic ketosis and cerebral metabolism. Ann Neurol 1978, 3:331-337.
-
(1978)
Ann Neurol
, vol.3
, pp. 331-337
-
-
DeVivo, D.C.1
Leckie, M.P.2
Ferrendelli, J.S.3
McDougal, D.B.4
-
26
-
-
0020591265
-
Effects of ketogenic diet on electroconvulsive threshold and brain contents of adenosine nucleotides
-
Nakazawa M., Kodama S., Matsuo T. Effects of ketogenic diet on electroconvulsive threshold and brain contents of adenosine nucleotides. Brain Dev 1983, 5:375-380.
-
(1983)
Brain Dev
, vol.5
, pp. 375-380
-
-
Nakazawa, M.1
Kodama, S.2
Matsuo, T.3
-
27
-
-
0033142036
-
Ketosis and epilepsy: 31P spectroscopic imaging at 4.1T
-
Pan J.W., Bebin E.M., Chu W.J., Hetherington H.P. Ketosis and epilepsy: 31P spectroscopic imaging at 4.1T. Epilepsia 1999, 40:703-707.
-
(1999)
Epilepsia
, vol.40
, pp. 703-707
-
-
Pan, J.W.1
Bebin, E.M.2
Chu, W.J.3
Hetherington, H.P.4
-
28
-
-
1642289587
-
The ketogenic diet increases mitochondrial uncoupling protein levels and activity
-
Sullivan P.G., Rippy N.A., Dorenbos K., Concepcion R.C., Agarwal A.K., Rho J.M. The ketogenic diet increases mitochondrial uncoupling protein levels and activity. Ann Neurol 2004, 55:576-580.
-
(2004)
Ann Neurol
, vol.55
, pp. 576-580
-
-
Sullivan, P.G.1
Rippy, N.A.2
Dorenbos, K.3
Concepcion, R.C.4
Agarwal, A.K.5
Rho, J.M.6
-
29
-
-
4644241829
-
A cDNA microarray analysis of gene expression profiles in rat hippocampus following a ketogenic diet
-
Noh H.S., Lee H.P., Kim D.W., Kang S.S., Cho G.J., Rho J.M., et al. A cDNA microarray analysis of gene expression profiles in rat hippocampus following a ketogenic diet. Mol Brain Res 2004, 129:80-87.
-
(2004)
Mol Brain Res
, vol.129
, pp. 80-87
-
-
Noh, H.S.1
Lee, H.P.2
Kim, D.W.3
Kang, S.S.4
Cho, G.J.5
Rho, J.M.6
-
30
-
-
70649089277
-
A ketogenic diet increases succinic dehydrogenase (SDH) activity and recovers age-related decrease in numeric density of SDH-positive mitochondria in cerebellar Purkinje cells of late-adult rats
-
Balietti M., Giorgetti B., Di Stefano G., Casoli T., Platano D., Solazzi M., et al. A ketogenic diet increases succinic dehydrogenase (SDH) activity and recovers age-related decrease in numeric density of SDH-positive mitochondria in cerebellar Purkinje cells of late-adult rats. Micron 2010, 41:143-148.
-
(2010)
Micron
, vol.41
, pp. 143-148
-
-
Balietti, M.1
Giorgetti, B.2
Di Stefano, G.3
Casoli, T.4
Platano, D.5
Solazzi, M.6
-
31
-
-
69149088651
-
A ketogenic diet increases succinic dehydrogenase activity in aging cardiomyocytes
-
Balietti M., Fattoretti P., Giorgetti B., Casoli T., Di Stefano G., Solazzi M., et al. A ketogenic diet increases succinic dehydrogenase activity in aging cardiomyocytes. Ann NY Acad Sci 2009, 1171:377-384.
-
(2009)
Ann NY Acad Sci
, vol.1171
, pp. 377-384
-
-
Balietti, M.1
Fattoretti, P.2
Giorgetti, B.3
Casoli, T.4
Di Stefano, G.5
Solazzi, M.6
-
32
-
-
48849092902
-
Induction of ketosis may improve mitochondrial function and decrease steady-state amyloid-β precursor protein (APP) levels in the aged dog
-
Studzinski C.M., MacKay W.A., Beckett T.L., Henderson S.T., Murphy M.P., Sullivan P.G., et al. Induction of ketosis may improve mitochondrial function and decrease steady-state amyloid-β precursor protein (APP) levels in the aged dog. Brain Res 2008, 1226:209-217.
-
(2008)
Brain Res
, vol.1226
, pp. 209-217
-
-
Studzinski, C.M.1
MacKay, W.A.2
Beckett, T.L.3
Henderson, S.T.4
Murphy, M.P.5
Sullivan, P.G.6
-
33
-
-
33746336630
-
Landau-Kleffner syndrome with mitochondrial respiratory chain-complex I deficiency
-
Kang H.-C., Kim H.D., Lee Y.M., Han S.H. Landau-Kleffner syndrome with mitochondrial respiratory chain-complex I deficiency. Pediatr Neurol 2006, 35:158-161.
-
(2006)
Pediatr Neurol
, vol.35
, pp. 158-161
-
-
Kang, H.-C.1
Kim, H.D.2
Lee, Y.M.3
Han, S.H.4
-
34
-
-
62149091063
-
Ketogenic diet in Alpers-Huttenlocher syndrome
-
Joshi C.N., Greenberg C.R., Mhanni A.A., Salman M.S. Ketogenic diet in Alpers-Huttenlocher syndrome. Pediatr Neurol 2009, 40:314-316.
-
(2009)
Pediatr Neurol
, vol.40
, pp. 314-316
-
-
Joshi, C.N.1
Greenberg, C.R.2
Mhanni, A.A.3
Salman, M.S.4
-
35
-
-
77649191276
-
A case of Ohtahara syndrome with mitochondrial respiratory chain complex I deficiency
-
Seo J.H., Lee Y.M., Lee J.S., Kim S.H., Kim H.D. A case of Ohtahara syndrome with mitochondrial respiratory chain complex I deficiency. Brain Dev 2010, 32:253-257.
-
(2010)
Brain Dev
, vol.32
, pp. 253-257
-
-
Seo, J.H.1
Lee, Y.M.2
Lee, J.S.3
Kim, S.H.4
Kim, H.D.5
-
36
-
-
41149085561
-
A ketogenic diet rescues the murine succinic semialdehyde dehydrogenase deficient phenotype
-
Nylen K., Velazquez J.L.P., Likhodii S.S., Cortez M.A., Shen L., Leshchenko Y., et al. A ketogenic diet rescues the murine succinic semialdehyde dehydrogenase deficient phenotype. Exp Neurol 2008, 210:449-457.
-
(2008)
Exp Neurol
, vol.210
, pp. 449-457
-
-
Nylen, K.1
Velazquez, J.L.P.2
Likhodii, S.S.3
Cortez, M.A.4
Shen, L.5
Leshchenko, Y.6
-
37
-
-
48249143179
-
The ketogenic diet increases mitochondrial glutathione levels
-
Jarrett S.G., Milder J.B., Liang L.-P., Patel M. The ketogenic diet increases mitochondrial glutathione levels. J Neurochem 2008, 106:1044-1051.
-
(2008)
J Neurochem
, vol.106
, pp. 1044-1051
-
-
Jarrett, S.G.1
Milder, J.B.2
Liang, L.-P.3
Patel, M.4
-
38
-
-
77955845526
-
Acute oxidative stress and systemic Nrf2 activation by the ketogenic diet
-
Milder J.B., Liang L.-P., Patel M. Acute oxidative stress and systemic Nrf2 activation by the ketogenic diet. Neurobiol Dis 2010, 40:238-244.
-
(2010)
Neurobiol Dis
, vol.40
, pp. 238-244
-
-
Milder, J.B.1
Liang, L.-P.2
Patel, M.3
-
39
-
-
33846852428
-
Ketones inhibit mitochondrial production of reactive oxygen species production following glutamate excitotoxicity by increasing NADH oxidation
-
Maalouf M., Sullivan P.G., Davis L., Kim D.Y., Rho J.M. Ketones inhibit mitochondrial production of reactive oxygen species production following glutamate excitotoxicity by increasing NADH oxidation. Neuroscience 2007, 145:256-264.
-
(2007)
Neuroscience
, vol.145
, pp. 256-264
-
-
Maalouf, M.1
Sullivan, P.G.2
Davis, L.3
Kim, D.Y.4
Rho, J.M.5
-
40
-
-
16044373842
-
Exon 1 of the HD gene with an expanded CAG repeat is sufficient to cause a progressive neurological phenotype in transgenic mice
-
Mangiarini L., Sathasivam K., Seller M., Cozens B., Harper A., Hetherington C., et al. Exon 1 of the HD gene with an expanded CAG repeat is sufficient to cause a progressive neurological phenotype in transgenic mice. Cell 1996, 87:493-506.
-
(1996)
Cell
, vol.87
, pp. 493-506
-
-
Mangiarini, L.1
Sathasivam, K.2
Seller, M.3
Cozens, B.4
Harper, A.5
Hetherington, C.6
-
41
-
-
34548095002
-
Metformin therapy in a transgenic mouse model of Huntington's disease
-
Ma T.C., Buescher J.L., Oatis B., Funk J.A., Nash A.J., Carrier R.L., et al. Metformin therapy in a transgenic mouse model of Huntington's disease. Neurosci Lett 2007, 411:98-103.
-
(2007)
Neurosci Lett
, vol.411
, pp. 98-103
-
-
Ma, T.C.1
Buescher, J.L.2
Oatis, B.3
Funk, J.A.4
Nash, A.J.5
Carrier, R.L.6
-
42
-
-
16244384501
-
A combination drug therapy improves cognition and reverses gene expression changes in a mouse model of Huntington's disease
-
Morton A.J., Hunt M.J., Hodges A.K., Lewis P.D., Redfern A.J., Dunnett S.B., et al. A combination drug therapy improves cognition and reverses gene expression changes in a mouse model of Huntington's disease. Eur J Neurosci 2005, 21:855-870.
-
(2005)
Eur J Neurosci
, vol.21
, pp. 855-870
-
-
Morton, A.J.1
Hunt, M.J.2
Hodges, A.K.3
Lewis, P.D.4
Redfern, A.J.5
Dunnett, S.B.6
-
43
-
-
77949431920
-
Responses to environmental enrichment differ with sex and genotype in a transgenic mouse model of Huntington's disease
-
Wood N.I., Carta V., Milde S., Skillings E.A., McAllister C.J., Ang Y.L.M., et al. Responses to environmental enrichment differ with sex and genotype in a transgenic mouse model of Huntington's disease. PLoS One 2010, 5:e9077.
-
(2010)
PLoS One
, vol.5
-
-
Wood, N.I.1
Carta, V.2
Milde, S.3
Skillings, E.A.4
McAllister, C.J.5
Ang, Y.L.M.6
-
44
-
-
0024311533
-
Nutritional evaluation of Huntington disease patients
-
Morales L.M., Estévez J., Suárez H., Villalobos R., Chacín de Bonilla L., Bonilla E. Nutritional evaluation of Huntington disease patients. Am J Clin Nutr 1989, 50:145-150.
-
(1989)
Am J Clin Nutr
, vol.50
, pp. 145-150
-
-
Morales, L.M.1
Estévez, J.2
Suárez, H.3
Villalobos, R.4
Chacín de Bonilla, L.5
Bonilla, E.6
-
45
-
-
0019796509
-
Body weight and dietary factors in Huntington's disease patients compared with matched controls
-
Sanberg P.R., Fibiger H.C., Mark R.F. Body weight and dietary factors in Huntington's disease patients compared with matched controls. Med J Aust 1981, 1:407-409.
-
(1981)
Med J Aust
, vol.1
, pp. 407-409
-
-
Sanberg, P.R.1
Fibiger, H.C.2
Mark, R.F.3
-
46
-
-
0037069280
-
Weight loss in early stage of Huntington's disease
-
Djoussé L., Knowlton B., Cupples L.A., Marder K., Shoulson I., Myers R.H. Weight loss in early stage of Huntington's disease. Neurology 2002, 59:1325-1330.
-
(2002)
Neurology
, vol.59
, pp. 1325-1330
-
-
Djoussé, L.1
Knowlton, B.2
Cupples, L.A.3
Marder, K.4
Shoulson, I.5
Myers, R.H.6
-
47
-
-
0026332133
-
Factors associated with slow progression in Huntington's disease
-
Myers R.H., Sax D.S., Koroshetz W.J., Mastromauro C., Cupples L.A., Kiely D.K., et al. Factors associated with slow progression in Huntington's disease. Arch Neurol 1991, 48:800-804.
-
(1991)
Arch Neurol
, vol.48
, pp. 800-804
-
-
Myers, R.H.1
Sax, D.S.2
Koroshetz, W.J.3
Mastromauro, C.4
Cupples, L.A.5
Kiely, D.K.6
-
48
-
-
0023742691
-
Conditions associated with Huntington's disease at death: a case-control study
-
Lanska D.J., Lanska M.J., Lavine L., Schoenberg B.S. Conditions associated with Huntington's disease at death: a case-control study. Arch Neurol 1988, 45:878-880.
-
(1988)
Arch Neurol
, vol.45
, pp. 878-880
-
-
Lanska, D.J.1
Lanska, M.J.2
Lavine, L.3
Schoenberg, B.S.4
-
49
-
-
0023026287
-
Correlates of early disability in Huntington's disease
-
Mayeux R., Stern Y., Herman A., Greenbaum L., Fahn S. Correlates of early disability in Huntington's disease. Ann Neurol 1986, 20:727-731.
-
(1986)
Ann Neurol
, vol.20
, pp. 727-731
-
-
Mayeux, R.1
Stern, Y.2
Herman, A.3
Greenbaum, L.4
Fahn, S.5
-
50
-
-
0029065482
-
Comparison of executive and visuospatial memory function in Huntington's disease and dementia of Alzheimer type matched for degree of dementia
-
Lange K.W., Sahakian B.J., Quinn N.P., Marsden C.D., Robbins T.W. Comparison of executive and visuospatial memory function in Huntington's disease and dementia of Alzheimer type matched for degree of dementia. J Neurol Neurosurg Psychiatry 1995, 58:598-606.
-
(1995)
J Neurol Neurosurg Psychiatry
, vol.58
, pp. 598-606
-
-
Lange, K.W.1
Sahakian, B.J.2
Quinn, N.P.3
Marsden, C.D.4
Robbins, T.W.5
-
51
-
-
0029906665
-
Executive and mnemonic functions in early Huntington's disease
-
Lawrence A.D., Sahakian B.J., Hodges J.R., Rosser A.E., Lange K.W., Robbins T.W. Executive and mnemonic functions in early Huntington's disease. Brain 1996, 119:1633-1645.
-
(1996)
Brain
, vol.119
, pp. 1633-1645
-
-
Lawrence, A.D.1
Sahakian, B.J.2
Hodges, J.R.3
Rosser, A.E.4
Lange, K.W.5
Robbins, T.W.6
-
52
-
-
33745979171
-
Differential effects of voluntary physical exercise on behavioral and brain-derived neurotrophic factor expression deficits in Huntington's disease transgenic mice
-
Pang T.Y.C., Stam N.C., Nithianantharajah J., Howard J.L., Hannan A.J. Differential effects of voluntary physical exercise on behavioral and brain-derived neurotrophic factor expression deficits in Huntington's disease transgenic mice. Neuroscience 2006, 141:569-584.
-
(2006)
Neuroscience
, vol.141
, pp. 569-584
-
-
Pang, T.Y.C.1
Stam, N.C.2
Nithianantharajah, J.3
Howard, J.L.4
Hannan, A.J.5
-
53
-
-
0033500593
-
Selective discrimination learning impairments in mice expressing the human Huntington's disease mutation
-
Lione L.A., Carter R.J., Hunt M.J., Bates G.P., Morton A.J., Dunnett S.B. Selective discrimination learning impairments in mice expressing the human Huntington's disease mutation. J Neurosci 1999, 19:10428-10437.
-
(1999)
J Neurosci
, vol.19
, pp. 10428-10437
-
-
Lione, L.A.1
Carter, R.J.2
Hunt, M.J.3
Bates, G.P.4
Morton, A.J.5
Dunnett, S.B.6
-
54
-
-
0037444426
-
Transgenic rat model of Huntington's disease
-
von Hörsten S., Schmitt I., Nguyen H.P., Holzmann C., Schmidt T., Walther T., et al. Transgenic rat model of Huntington's disease. Hum Mol Genet 2003, 12:617-624.
-
(2003)
Hum Mol Genet
, vol.12
, pp. 617-624
-
-
von Hörsten, S.1
Schmitt, I.2
Nguyen, H.P.3
Holzmann, C.4
Schmidt, T.5
Walther, T.6
-
55
-
-
0028234787
-
CAG repeat size and clinical presentation in Huntington's disease
-
Ashizawa T., Wong L.-J.C., Richards C.S., Caskey C.T., Jankovic J. CAG repeat size and clinical presentation in Huntington's disease. Neurology 1994, 44:1137-1143.
-
(1994)
Neurology
, vol.44
, pp. 1137-1143
-
-
Ashizawa, T.1
Wong, L.-J.C.2
Richards, C.S.3
Caskey, C.T.4
Jankovic, J.5
-
56
-
-
0027240431
-
Trinucleotide repeat length instability and age of onset in Huntington's disease
-
Duyao M., Ambrose C., Myers R., Novelletto A., Persichetti F., Frontali M., et al. Trinucleotide repeat length instability and age of onset in Huntington's disease. Nat Gen 1993, 4:387-392.
-
(1993)
Nat Gen
, vol.4
, pp. 387-392
-
-
Duyao, M.1
Ambrose, C.2
Myers, R.3
Novelletto, A.4
Persichetti, F.5
Frontali, M.6
-
57
-
-
67349261223
-
Improvement in motor and exploratory behavior in Rett syndrome mice with restricted ketogenic and standard diets
-
Mantis J.G., Fritz C.L., Marsh J., Heinrichs S.C., Seyfried T.N. Improvement in motor and exploratory behavior in Rett syndrome mice with restricted ketogenic and standard diets. Epilepsy Behav 2009, 15:133-141.
-
(2009)
Epilepsy Behav
, vol.15
, pp. 133-141
-
-
Mantis, J.G.1
Fritz, C.L.2
Marsh, J.3
Heinrichs, S.C.4
Seyfried, T.N.5
-
58
-
-
77952347202
-
FGF21 is dispensable for hypothermia induced by fasting in mice
-
Oishi K., Sakamoto K., Konishi M., Murata Y., Itoh N., Sei H. FGF21 is dispensable for hypothermia induced by fasting in mice. Neuroendocrinol Lett 2010, 31:101-105.
-
(2010)
Neuroendocrinol Lett
, vol.31
, pp. 101-105
-
-
Oishi, K.1
Sakamoto, K.2
Konishi, M.3
Murata, Y.4
Itoh, N.5
Sei, H.6
-
59
-
-
77954616718
-
Dietary supplementation with medium-chain TAG has long-lasting cognition-enhancing effects in aged dogs
-
Pan Y., Larson B., Araujo J.A., Lau W., de Rivera C., Santana R., et al. Dietary supplementation with medium-chain TAG has long-lasting cognition-enhancing effects in aged dogs. Br J Nutr 2010, 103:1746-1754.
-
(2010)
Br J Nutr
, vol.103
, pp. 1746-1754
-
-
Pan, Y.1
Larson, B.2
Araujo, J.A.3
Lau, W.4
de Rivera, C.5
Santana, R.6
-
60
-
-
77949888384
-
Diet-induced ketosis improves cognitive performance in aged rats
-
Xu K., Sun X., Eroku B.O., Tsipis C.P., Puchowicz M.A., LaManna J.C. Diet-induced ketosis improves cognitive performance in aged rats. Adv Exp Biol Med 2010, 662:71-75.
-
(2010)
Adv Exp Biol Med
, vol.662
, pp. 71-75
-
-
Xu, K.1
Sun, X.2
Eroku, B.O.3
Tsipis, C.P.4
Puchowicz, M.A.5
LaManna, J.C.6
-
61
-
-
0034731403
-
Timing of ketogenic diet initiation in an experimental epilepsy model
-
Su S.W., Sogawa M.R.C.Y., Silveira D.C., Holmes G.L., Stafstrom C.E. Timing of ketogenic diet initiation in an experimental epilepsy model. Dev Brain Res 2000, 125:131-138.
-
(2000)
Dev Brain Res
, vol.125
, pp. 131-138
-
-
Su, S.W.1
Sogawa, M.R.C.Y.2
Silveira, D.C.3
Holmes, G.L.4
Stafstrom, C.E.5
-
62
-
-
1242342179
-
Detrimental effects of the ketogenic diet on cognitive function in rats
-
Zhao Q., Stafstrom C.E., Fu D.D., Hu Y., Holmes G.L. Detrimental effects of the ketogenic diet on cognitive function in rats. Pediatr Res 2004, 55:498-506.
-
(2004)
Pediatr Res
, vol.55
, pp. 498-506
-
-
Zhao, Q.1
Stafstrom, C.E.2
Fu, D.D.3
Hu, Y.4
Holmes, G.L.5
-
63
-
-
32844469101
-
Transitory gliosis in the CA3 hippocampal region in rats fed on a ketogenic diet
-
Silva M.C., Rocha J., Pires C.S., Ribeiro L.C., Brolese G., Leite M.C., et al. Transitory gliosis in the CA3 hippocampal region in rats fed on a ketogenic diet. Nutr Neurosci 2005, 8:259-264.
-
(2005)
Nutr Neurosci
, vol.8
, pp. 259-264
-
-
Silva, M.C.1
Rocha, J.2
Pires, C.S.3
Ribeiro, L.C.4
Brolese, G.5
Leite, M.C.6
-
64
-
-
0033878303
-
The ketogenic diet inhibits epileptogenesis in EL mice: a genetic model for idiopathic epilepsy
-
Todorova M.T., Tandon P., Madore R.A., Stafstrom C.E., Seyfried T.N. The ketogenic diet inhibits epileptogenesis in EL mice: a genetic model for idiopathic epilepsy. Epilepsia 2000, 41:933-940.
-
(2000)
Epilepsia
, vol.41
, pp. 933-940
-
-
Todorova, M.T.1
Tandon, P.2
Madore, R.A.3
Stafstrom, C.E.4
Seyfried, T.N.5
-
65
-
-
0030756197
-
Ketogenic diet: effects on expression of kindled seizures and behavior in adult rats
-
Hori A., Tandon P., Holmes G.L., Stafstrom C.E. Ketogenic diet: effects on expression of kindled seizures and behavior in adult rats. Epilepsia 1997, 38:750-758.
-
(1997)
Epilepsia
, vol.38
, pp. 750-758
-
-
Hori, A.1
Tandon, P.2
Holmes, G.L.3
Stafstrom, C.E.4
-
67
-
-
70449640557
-
Long-term effects of a very low-carbohydrate diet and a low-fat diet on mood and cognitive function
-
Brinkworth G.D., Buckley J.D., Noakes M., Clifton P.M., Wilson C.J. Long-term effects of a very low-carbohydrate diet and a low-fat diet on mood and cognitive function. Arch Int Med 2009, 169:1873-1880.
-
(2009)
Arch Int Med
, vol.169
, pp. 1873-1880
-
-
Brinkworth, G.D.1
Buckley, J.D.2
Noakes, M.3
Clifton, P.M.4
Wilson, C.J.5
-
68
-
-
34548706522
-
Low- and high-carbohydrate weight-loss diets have similar effects on mood but not cognitive performance
-
Halyburton A.K., Brinkworth G.D., Wilson C.J., Noakes M., Buckley J.D., Keogh J.B., et al. Low- and high-carbohydrate weight-loss diets have similar effects on mood but not cognitive performance. Am J Clin Nutr 2007, 86:580-587.
-
(2007)
Am J Clin Nutr
, vol.86
, pp. 580-587
-
-
Halyburton, A.K.1
Brinkworth, G.D.2
Wilson, C.J.3
Noakes, M.4
Buckley, J.D.5
Keogh, J.B.6
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