A Drosophila model of GSS syndrome suggests defects in active zones are responsible for pathogenesis of GSS syndrome

Human Molecular Genetics

Volumn 19, Issue 22, 2010, Pages 4474-4489

  Choi, Jin Kyu ^a   Jeon, Yong Chul ^a   Lee, Dae Weon ^a   Oh, Jae Min ^a   Lee, Hyun Pil ^a   Jeong, Byung Hoon ^a   Carp, Richard I ^b   Koh, Young Ho ^a   Kim, Yong Sun ^a  

^a Hallym University   (South Korea)

^b NEW YORK STATE INSTITUTE FOR BASIC RESEARCH IN DEVELOPMENTAL DISABILITIES   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

BIOLOGICAL MARKER; CASPASE 3; GLUTAMIC ACID; LEUCINE; PRION PROTEIN; PROTEIN ELKS; UNCLASSIFIED DRUG;

AMINO ACID SUBSTITUTION; ANIMAL EXPERIMENT; ANIMAL MODEL; APOPTOSIS; ARTICLE; CLIMBING; CONTROLLED STUDY; DEATH; DROSOPHILA; FEMALE; FLY; GERSTMANN STRAUSSLER SCHEINKER SYNDROME; LARVA; MOUSE; NERVE CELL NECROSIS; NEUROMUSCULAR SYNAPSE; NONHUMAN; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN GLYCOSYLATION; PROTEIN LOCALIZATION; SCRAPIE; SIGNAL TRANSDUCTION; SYNAPSE; WILD TYPE;

ANIMALS; BRAIN; DISEASE MODELS, ANIMAL; DROSOPHILA; FEMALE; GERSTMANN-STRAUSSLER-SCHEINKER DISEASE; HUMANS; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; PRIONS;

MUS;

EID: 77958462553     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddq379     Document Type: Article

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