Primary immunodeficiencies

Journal of Allergy and Clinical Immunology

Volumn 125, Issue 2 SUPPL. 2, 2010, Pages

  Notarangelo, Luigi D ^a  

^a BOSTON CHILDREN S HOSPITAL   (United States)

Author keywords

antibody deficiency; gene therapy; hematopoietic cell transplantation; immunoglobulin replacement therapy; innate immunity defects; Primary immunodeficiency; T cell immunodeficiency

Indexed keywords

ACTIVATION INDUCED CYTIDINE DEAMINASE; ADENOSINE DEAMINASE; ADENYLATE KINASE; ANTIFUNGAL AGENT; B LYMPHOCYTE RECEPTOR; COTRIMOXAZOLE; CYTOMEGALOVIRUS VACCINE; DIHYDRORHODAMINE 123; FORKHEAD TRANSCRIPTION FACTOR; GAMMA INTERFERON; GLYCOSIDASE; IMMUNOGLOBULIN; IMMUNOGLOBULIN G; INTERLEUKIN 1 RECEPTOR ASSOCIATED KINASE; INTERLEUKIN 15; INTERLEUKIN 2; INTERLEUKIN 4; INTERLEUKIN 7; INTERLEUKIN 9; JANUS KINASE; L SELECTIN; MANNOSE BINDING LECTIN; RAG2 PROTEIN; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE PHOSPHATE; STAT PROTEIN; T LYMPHOCYTE RECEPTOR; TOLL LIKE RECEPTOR; UNCLASSIFIED DRUG; UNINDEXED DRUG; URACIL N GLYCOSIDASE; WISKOTT ALDRICH SYNDROME PROTEIN;

ANTIBODY RESPONSE; ARTICLE; AUTOSOMAL RECESSIVE INHERITANCE; CELL TRANSPLANTATION; CHRONIC DIARRHEA; CHRONIC GRANULOMATOUS DISEASE; CLINICAL FEATURE; COMBINED IMMUNODEFICIENCY; COMMON VARIABLE IMMUNODEFICIENCY; CYTOMEGALOVIRUS; CYTOMEGALOVIRUS INFECTION; CYTOTOXICITY; DRUG MEGADOSE; ENZYME DEFICIENCY; ENZYME REPLACEMENT; FAILURE TO THRIVE; GENE IDENTIFICATION; GENE MUTATION; GENE THERAPY; GENETIC CODE; GRAFT VERSUS HOST REACTION; HEMATOPOIETIC CELL; HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS; HUMAN; IMMUNE DEFICIENCY; IMMUNE DYSREGULATION; IMMUNOGLOBULIN A DEFICIENCY; IMMUNOSUPPRESSIVE TREATMENT; INNATE IMMUNITY; LEUKOCYTE ADHESION DEFICIENCY; LYMPHOCYTIC INFILTRATION; MOLECULAR GENETICS; MYCOSIS; NUTRITIONAL SUPPORT; OMENN SYNDROME; PATHOPHYSIOLOGY; PHAGOCYTE; PNEUMOCYSTIS JIROVECI; PNEUMOCYSTIS PNEUMONIA; PNEUMONIA; PRIMARY IMMUNE DEFICIENCY; PRIORITY JOURNAL; PROPHYLAXIS; PROTEIN EXPRESSION; RASH; SEVERE COMBINED IMMUNODEFICIENCY; SPLENOMEGALY; T LYMPHOCYTE; UMBILICAL CORD BLOOD; UNSPECIFIED SIDE EFFECT; VIRUS INFECTION; WISKOTT ALDRICH SYNDROME; X LINKED AGAMMAGLOBULINEMIA;

ANIMALS; GENE THERAPY; GENETIC PREDISPOSITION TO DISEASE; GENETIC TESTING; HEMATOPOIETIC STEM CELL TRANSPLANTATION; HUMANS; IMMUNITY, CELLULAR; IMMUNITY, INNATE; IMMUNOGLOBULINS, INTRAVENOUS; IMMUNOLOGIC DEFICIENCY SYNDROMES; INFANT, NEWBORN; POLYMORPHISM, GENETIC;

EID: 76749147849     PISSN: 00916749     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.jaci.2009.07.053     Document Type: Article

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