Update in understanding common variable immunodeficiency disorders (CVIDs) and the management of patients with these conditions

British Journal of Haematology

Volumn 145, Issue 6, 2009, Pages 709-727

  Chapel, Helen ^a,b   Cunningham Rundles, Charlotte ^c  

^a JOHN RADCLIFFE HOSPITAL   (United Kingdom)

^b UNIVERSITY OF OXFORD   (United Kingdom)

^c MOUNT SINAI SCHOOL OF MEDICINE   (United States)

Author keywords

Antibody failure; Clinical phenotypes; Common variable immune deficiency disorders; Genetic findings; Management of patients

Indexed keywords

AZATHIOPRINE; BUDESONIDE; CORTICOSTEROID; CYCLOSPORIN A; HYDROXYCHLOROQUINE; IMMUNOGLOBULIN; IMMUNOGLOBULIN G; IMMUNOSUPPRESSIVE AGENT; MERCAPTOPURINE; METHOTREXATE; MYCOPHENOLIC ACID 2 MORPHOLINOETHYL ESTER; RITUXIMAB;

AUTOIMMUNE DISEASE; CLINICAL FEATURE; COMMON VARIABLE IMMUNODEFICIENCY; DOSE RESPONSE; DRUG DOSE REDUCTION; GENE MUTATION; GENETIC DISORDER; GRANULOMA; HUMAN; IMMUNOGLOBULIN PRODUCTION; INFECTION COMPLICATION; INFLAMMATION; INTERSTITIAL PNEUMONIA; LYMPHOCYTIC INFILTRATION; LYMPHOPROLIFERATIVE DISEASE; PATHOGENESIS; PHENOTYPE; PREVALENCE; PRIORITY JOURNAL; PROGNOSIS; REVIEW; UNSPECIFIED SIDE EFFECT;

AGE OF ONSET; COMMON VARIABLE IMMUNODEFICIENCY; HUMANS; IMMUNOGLOBULIN G; IMMUNOGLOBULINS, INTRAVENOUS; POLYMORPHISM, GENETIC; SURVIVAL RATE;

EID: 66749092909     PISSN: 00071048     EISSN: 13652141     Source Type: Journal    
DOI: 10.1111/j.1365-2141.2009.07669.x     Document Type: Review

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