Tissue-specific cytochrome c oxidase assembly defects due to mutations in SCO2 and SURF1

Biochemical Journal

Volumn 392, Issue 3, 2005, Pages 625-632

  Stiburek, Lukas ^a   Vesela, Katerina ^a   Hansikova, Hana ^a   Pecina, Petr ^b   Tesarova, Marketa ^a   Cerna, Leona ^a   Houstek, Josef ^b   Zeman, Jiri ^a  

^a CHARLES UNIVERSITY   (Czech Republic)

^b INSTITUTE OF PHYSIOLOGY   (Czech Republic)

Author keywords

Assembly pathway; CuA centre; Cytochrome c oxidase; Mitochondria; SCO2; SURF1

Indexed keywords

BRAIN; IMMUNOLOGY; MUTAGENESIS; PATIENT MONITORING; PROTEINS; TISSUE;

ASSEMBLY PATHWAY; CUA CENTRE; CYTOCHROME C OXIDASE; MITOCHONDRIA; SCO2; SURF1;

PIGMENTS;

COPPER; CYTOCHROME C OXIDASE; CYTOCHROME C1; CYTOCHROME C4; HOLOENZYME; MEMBRANE PROTEIN; UNCLASSIFIED DRUG;

ARTICLE; BRAIN TISSUE; CELL NUCLEUS; COMPLEX FORMATION; ENZYME SUBUNIT; GEL; GENE MUTATION; HEART; HUMAN; HUMAN TISSUE; IMMUNOBLOTTING; PATIENT; PRIORITY JOURNAL; SKELETAL MUSCLE; STEADY STATE; TISSUE SPECIFICITY;

BRAIN; CARRIER PROTEINS; CHILD, PRESCHOOL; ELECTRON TRANSPORT COMPLEX IV; FIBROBLASTS; GENE EXPRESSION REGULATION, ENZYMOLOGIC; HUMANS; INFANT; LIVER; MEMBRANE PROTEINS; MITOCHONDRIAL PROTEINS; MUSCLE, SKELETAL; MUTATION; MYOCARDIUM; ORGAN SPECIFICITY; PROTEIN SUBUNITS; PROTEINS;

EUKARYOTA;

EID: 29644440471     PISSN: 02646021     EISSN: None     Source Type: Journal    
DOI: 10.1042/BJ20050807     Document Type: Article

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